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Open Access 13-02-2024 | Hydrocephalus | Case report

Corticosteroid treatment for acute hydrocephalus in neurosarcoidosis: a case report

Authors: Edoardo Dalmato Schilke, Giulia Remoli, Claudia Cutellé, Claudia Balducci, Diletta Cereda, Maria Letizia Fusco, Lucio Tremolizzo, Carlo Ferrarese, Ildebrando Appollonio, Maura Frigo

Published in: Journal of Medical Case Reports | Issue 1/2024

Abstract

Background

Neurosarcoidosis occurs symptomatically in 5–10% of patients with sarcoidosis, and hydrocephalus is a rare complication of neurosarcoidosis, with either acute or subacute onset and presenting symptoms related to increased intracranial pressure. It represents a potentially fatal manifestation with a mortality rate of 22% (increased to 75% in case of coexistence of seizures) that requires a prompt initiation of treatment. High-dose intravenous corticosteroid treatment and neurosurgical treatment must be considered in all cases of neurosarcoidosis hydrocephalus.

Case presentation

Here we present a case of hydrocephalus in neurosarcoidosis, complicated by generalized seizures, in a 29-year-old Caucasian male patient treated with medical treatment only, with optimal response.

Conclusion

Since neurosurgery treatment can lead to severe complications, this case report underlines the possibility to undergo only medical treatment in selected cases. Further studies are needed to stratify patients and better identify those eligible for only medical approach.

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Title: Corticosteroid treatment for acute hydrocephalus in neurosarcoidosis: a case report
Authors: Edoardo Dalmato Schilke
Giulia Remoli
Claudia Cutellé
Claudia Balducci
Diletta Cereda
Maria Letizia Fusco
Lucio Tremolizzo
Carlo Ferrarese
Ildebrando Appollonio
Maura Frigo
Publication date: 13-02-2024
Publisher: BioMed Central
Keywords: Hydrocephalus
Sarcoidosis
Disease of Central Nervous System
Published in: Journal of Medical Case Reports / Issue 1/2024
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/s13256-024-04359-9

Keynote webinar | Spotlight on sleep in brain health

Springer Medicine

Corticosteroid treatment for acute hydrocephalus in neurosarcoidosis: a case report

Abstract

Background

Case presentation

Conclusion

Keynote webinar | Spotlight on sleep in brain health

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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