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Acta Neuropathologica

Issue 4/2019

Content (14 Articles)

Creutzfeldt-Jakob Disease Commentary Letter

Alpha-synuclein: prion or prion-like?

Rehana K. Leak, Matthew P. Frosch, Thomas G. Beach, Glenda M. Halliday

Open Access Pathology Original Paper

Oral and intravenous transmission of α-synuclein fibrils to mice

Stephanie Lohmann, Maria E. Bernis, Babila J. Tachu, Alexandra Ziemski, Jessica Grigoletto, Gültekin Tamgüney

Open Access Pathology Original Paper

Evidence for bidirectional and trans-synaptic parasympathetic and sympathetic propagation of alpha-synuclein in rats

Nathalie Van Den Berge, Nelson Ferreira, Hjalte Gram, Trine Werenberg Mikkelsen, Aage Kristian Olsen Alstrup, Nicolas Casadei, Pai Tsung-Pin, Olaf Riess, Jens Randel Nyengaard, Gültekin Tamgüney, Poul Henning Jensen, Per Borghammer

Open Access Dementia Original Paper

Tau is required for progressive synaptic and memory deficits in a transgenic mouse model of α-synucleinopathy

Balvindar Singh, Ana Covelo, Héctor Martell-Martínez, Carmen Nanclares, Mathew A. Sherman, Emmanuel Okematti, Joyce Meints, Peter J. Teravskis, Christopher Gallardo, Alena V. Savonenko, Michael A. Benneyworth, Sylvain E. Lesné, Dezhi Liao, Alfonso Araque, Michael K. Lee

Open Access Parkinson's Disease Original Paper

Depopulation of dense α-synuclein aggregates is associated with rescue of dopamine neuron dysfunction and death in a new Parkinson’s disease model

Michal Wegrzynowicz, Dana Bar-On, Laura Calo’, Oleg Anichtchik, Mariangela Iovino, Jing Xia, Sergey Ryazanov, Andrei Leonov, Armin Giese, Jeffrey W. Dalley, Christian Griesinger, Uri Ashery, Maria Grazia Spillantini

Alzheimer's Disease Original Paper

Alzheimer’s disease clinical variants show distinct regional patterns of neurofibrillary tangle accumulation

Cathrine Petersen, Amber L. Nolan, Elisa de Paula França Resende, Zachary Miller, Alexander J. Ehrenberg, Maria Luisa Gorno-Tempini, Howard J. Rosen, Joel H. Kramer, Salvatore Spina, Gil D. Rabinovici, Bruce L. Miller, William W. Seeley, Helmut Heinsen, Lea Tenenholz Grinberg

Alzheimer's Disease Original Paper

Impact of TREM2 risk variants on brain region-specific immune activation and plaque microenvironment in Alzheimer’s disease patient brain samples

Stefan Prokop, Kelly R. Miller, Sergio R. Labra, Rose M. Pitkin, Kevt’her Hoxha, Sneha Narasimhan, Lakshmi Changolkar, Alyssa Rosenbloom, Virginia M.-Y. Lee, John Q. Trojanowski

Open Access Alzheimer's Disease Original Paper

BIN1 recovers tauopathy-induced long-term memory deficits in mice and interacts with Tau through Thr348 phosphorylation

Maxime Sartori, Tiago Mendes, Shruti Desai, Alessia Lasorsa, Adrien Herledan, Nicolas Malmanche, Petra Mäkinen, Mikael Marttinen, Idir Malki, Julien Chapuis, Amandine Flaig, Anaïs-Camille Vreulx, Marion Ciancia, Philippe Amouyel, Florence Leroux, Benoit Déprez, François-Xavier Cantrelle, Damien Maréchal, Laurent Pradier, Mikko Hiltunen, Isabelle Landrieu, Devrim Kilinc, Yann Herault, Jocelyn Laporte, Jean-Charles Lambert

Open Access Encephalitis Original Paper

The neuropathology of fatal encephalomyelitis in human Borna virus infection

Friederike Liesche, Viktoria Ruf, Saida Zoubaa, Gwendolyn Kaletka, Marco Rosati, Dennis Rubbenstroth, Christiane Herden, Lutz Goehring, Silke Wunderlich, Miguel Frederic Wachter, Georg Rieder, Ines Lichtmannegger, Willibald Permanetter, Josef G. Heckmann, Klemens Angstwurm, Bernhard Neumann, Bruno Märkl, Stefan Haschka, Hans-Helmut Niller, Barbara Schmidt, Jonathan Jantsch, Christoph Brochhausen, Kore Schlottau, Arnt Ebinger, Bernhard Hemmer, Markus J. Riemenschneider, Jochen Herms, Martin Beer, Kaspar Matiasek, Jürgen Schlegel

Open Access Pathology Correspondence

Dipeptide repeat (DPR) pathology in the skeletal muscle of ALS patients with C9ORF72 repeat expansion

Matthew D. Cykowski, Dennis W. Dickson, Suzanne Z. Powell, Anithachristy S. Arumanayagam, Andreana L. Rivera, Stanley H. Appel

Alzheimer's Disease Correspondence

Controversies about the subcellular localization and mechanisms of action of the Alzheimer's disease-protective CD33 splice variant

Sudeshna Saha, Shoib S. Siddiqui, Naazneen Khan, Andrea Verhagen, Weiping Jiang, Stevan Springer, Pradipta Ghosh, Ajit Varki

Open Access Correction

Correction to: Ketogenic diet ameliorates axonal defects and promotes myelination in Pelizaeus–Merzbacher disease

Sina K. Stumpf, Stefan A. Berghoff, Andrea Trevisiol, Lena Spieth, Tim Düking, Lennart V. Schneider, Lennart Schlaphoff, Steffi Dreha-Kulaczewski, Annette Bley, Dinah Burfeind, Kathrin Kusch, Miso Mitkovski, Torben Ruhwedel, Philipp Guder, Heiko Röhse, Jonas Denecke, Jutta Gärtner, Wiebke Möbius, Klaus-Armin Nave, Gesine Saher

Correction

Correction to: Endogenous oligodendroglial alpha-synuclein and TPPP/p25α orchestrate alpha-synuclein pathology in experimental multiple system atrophy models

Panagiota Mavroeidi, Fedra Arvanitaki, Anastasia-Kiriaki Karakitsou, Maria Vetsi, Ismini Kloukina, Markus Zweckstetter, Karin Giller, Stefan Becker, Zachary A. Sorrentino, Benoit I. Giasson, Poul Henning Jensen, Leonidas Stefanis, Maria Xilouri