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Child's Nervous System
Published in: Child's Nervous System 11/2020

01-11-2020 | Spina Bifida Aperta | Case-Based Review

Cervical myelomeningocele with CSF leakage: a case-based review

Authors: Kevin Armas-Melián, Sara Iglesias, Bienvenido Ros, María Isabel Martínez-León, Miguel Ángel Arráez

Published in: Child's Nervous System | Issue 11/2020

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Abstract

Background

The cystic spinal dysraphism of the cervical and upper thoracic region (CDCT) accounts for only 3.9 to 8% of spina bifida cystica lesions. The presence of external cerebrospinal fluid (CSF) leakage is infrequent and very few authors have reported about surgical complications.

Case report

We present the case of a new born diagnosed of CDCT C1-C3 with a stalk of fibrovascular tissue, CSF leakage, hydrocephalus, and type Chiari II malformation, discuss about the chosen surgical technique and the associated complications, and make a review of the literature focusing on the main aspects of CDCT.

Conclusions

The CDCT with a stalk of neuroglial and/or fibrovascular tissue originates from the dorsal surface of the spinal cord and penetrates into a cervical cystic sac. The presence of CSF leakage, hydrocephalus, and/or type Chiari II malformation can influence to decide the most appropriate surgical technique.
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Metadata
Title
Cervical myelomeningocele with CSF leakage: a case-based review
Authors
Kevin Armas-Melián
Sara Iglesias
Bienvenido Ros
María Isabel Martínez-León
Miguel Ángel Arráez
Publication date
01-11-2020
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 11/2020
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-020-04743-y

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