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Pediatric Nephrology

Issue 10/2021

Content (41 Articles)

Open Access Rituximab Editorial Commentary

Commentary on “Pediatric Idiopathic Steroid-sensitive Nephrotic Syndrome Diagnosis and Therapy - Short version of the updated German Best Practice Guideline (S2e)”

Rasmus Ehren, Marcus R. Benz, Paul T. Brinkkötter, Jörg Dötsch, Wolfgang R. Eberl, Jutta Gellermann, Peter F. Hoyer, Isabelle Jordans, Clemens Kamrath, Markus J. Kemper, Kay Latta, Dominik Müller, Jun Oh, Burkhard Tönshoff, Stefanie Weber, Lutz T. Weber

Open Access Nephrotic Syndrome Guidelines

Pediatric idiopathic steroid-sensitive nephrotic syndrome: diagnosis and therapy —short version of the updated German best practice guideline (S2e) — AWMF register no. 166-001, 6/2020

Rasmus Ehren, Marcus R. Benz, Paul T. Brinkkötter, Jörg Dötsch, Wolfgang R. Eberl, Jutta Gellermann, Peter F. Hoyer, Isabelle Jordans, Clemens Kamrath, Markus J. Kemper, Kay Latta, Dominik Müller, Jun Oh, Burkhard Tönshoff, Stefanie Weber, Lutz T. Weber

Open Access Tuberculosis Review

Preventing tuberculosis in paediatric kidney transplant recipients: is there a role for BCG immunisation pre-transplantation in low tuberculosis incidence countries?

Alasdair Bamford, Garth Dixon, Nigel Klein, Stephen D. Marks, Nicole Ritz, Steven B. Welch, Marc Tebruegge

Open Access IgA Vasculitis Systematic Review/Meta-analysis

A systematic review of urine biomarkers in children with IgA vasculitis nephritis

Chloe E. C. Williams, Aileen Toner, Rachael D. Wright, Louise Oni

Chronic Kidney Disease Educational Review

Familial hypomagnesemia with hypercalciuria and nephrocalcinosis

Mònica Vall-Palomar, Leire Madariaga, Gema Ariceta

Lisinopril Educational Review

Non-immunosuppressive therapies for childhood IgA nephropathy

Yuko Shima, Koichi Nakanishi, Norishige Yoshikawa

Kidney Transplantation Educational Review

Oral health in children with chronic kidney disease

Elizabeth Velan, Barbara Sheller

Kidney Transplantation Educational Review

Emerging monitoring technologies in kidney transplantation

Abdulla Ehlayel, K’joy J. A. Simms, Isa F. Ashoor

Edema Clinical Quiz

An unusual disease mimicking congenital nephrotic syndrome: Questions

Nurdan Yıldız, Mehtap Sak, Sabahat Inanır, Bilge Sahin Akkelle, Harika Alpay

Edema Clinical Quiz

An unusual disease mimicking congenital nephrotic syndrome: Answers

Nurdan Yıldız, Mehtap Sak, Sabahat Inanır, Bilge Sahin Akkelle, Harika Alpay

Hypoparathyroidism Clinical Quiz

Hypocalcemia not related to chronic kidney disease: Answers

Cengiz Zeybek, Onur Akin, Ahmet Bolat

Acute Kidney Injury Clinical Quiz

A 17-year-old boy with progressive abdominal pain: Questions

Olivia Gilbert, Mingshan Lai, Jessica Zagory, Randall Craver, Amanda Messer, Isa F. Ashoor

IgA Vasculitis Clinical Quiz

A 17-year-old boy with progressive abdominal pain: Answers

Olivia Gilbert, Mingshan Lai, Jessica Zagory, Randall Craver, Amanda Messer, Isa F. Ashoor

Rickets Clinical Quiz

A 5-year-old girl with bony deformities and disproportionate short stature: Questions

Rangaswamy Darshan, Sriram Krishnamurthy, Bobbity Deepthi, Pediredla Karunakar, Aakash Chandran Chidambaram, Arumugom Archana

A 5-year-old girl with bony deformities and disproportionate short stature: Answers

Rangaswamy Darshan, Sriram Krishnamurthy, Bobbity Deepthi, Pediredla Karunakar, Aakash Chandran Chidambaram, Arumugom Archana

Kidney Transplantation Original Article

Long-term complications of systemic oxalosis in children—a retrospective single-center cohort study

Efrat Ben-Shalom, Ruth Cytter-Kuint, Choni Rinat, Rachel Becker-Cohen, Shimrit Tzvi-Behr, Jenny Goichberg, Vardit Peles, Yaacov Frishberg

Acidosis Original Article

Molecular aspects and long-term outcome of patients with primary distal renal tubular acidosis

Sara Gómez-Conde, Alejandro García-Castaño, Mireia Aguirre, María Herrero, Leire Gondra, Nélida García-Pérez, Paula García-Ledesma, Luis Martín-Penagos, Cecilia Dall’Anese, Gema Ariceta, Luis Castaño, Leire Madariaga

Original Article

Congenital anomalies of the kidney and urinary tract in a cohort of 280 consecutive patients with Hirschsprung disease

Alessio Pini Prato, Rossella Arnoldi, Ilaria Falconi, Maria Pia Dusio, Isabella Ceccherini, Augusta Tentori, Enrico Felici, Paolo Nozza

Albuminuria Original Article

The spectrum of kidney function alterations in adolescents with a solitary functioning kidney

Mathilde Grapin, François Gaillard, Nathalie Biebuyck, Melissa Ould-Rabah, Carole Hennequin, Romain Berthaud, Guillaume Dorval, Thomas Blanc, Maryvonne Hourmant, Nassim Kamar, Lionel Rostaing, Lionel Couzi, Nicolas Garcelon, Dominique Prié, Olivia Boyer, Frank Bienaimé

Peritonitis Original Article

Structured re-training to reduce peritonitis in a pediatric peritoneal dialysis program: a quality improvement intervention

Sharon Teo, Tin Wei Yuen, Clarissa Wei-Shuen Cheong, Md Azizur Rahman, Neha Bhandari, Noor-Haziah Hussain, Hamidah Mistam, Jing Geng, Charmaine Yan-Pin Goh, Mya Than, Yiong-Huak Chan, Hui-Kim Yap, Kar-Hui Ng

Open Access Losartan Original Article

Effects of losartan and enalapril on serum uric acid and GFR in children with proteinuria

Charlotte E. Bryant, Azita Rajai, Nicholas J. A. Webb, Ronald J. Hogg

Erythropoietin Original Article

Associations among erythropoietic, iron-related, and FGF23 parameters in pediatric kidney transplant recipients

Blair Limm-Chan, Katherine Wesseling-Perry, Meghan H. Pearl, Grace Jung, Eileen Tsai-Chambers, Patricia L. Weng, Mark R. Hanudel

Heart Surgery Original Article

Serum metabolic profile of postoperative acute kidney injury following infant cardiac surgery with cardiopulmonary bypass

Jesse A. Davidson, Benjamin S. Frank, Tracy T. Urban, Mark Twite, James Jaggers, Ludmila Khailova, Jelena Klawitter

Early relapse of atypical hemolytic uremic syndrome following ABO-incompatible living–related pediatric kidney re-transplant successfully treated with eculizumab

Jelena Stojanovic, Anna Adamusiak, Aoife Waters, Neil J. Sebire, Nicos Kessaris, Nizam Mamode, Stephen D. Marks

Open Access Crohn's Disease Brief Report

Atypical HUS and Crohn’s disease—interference of intestinal disease activity with complement-blocking treatment

Orsolya Horváth, Kata Kelen, Zoltán Prohászka, Ádám Hosszú, Attila J Szabó, George S Reusz