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Published in: Autoimmunity Highlights 1/2019

Open Access 01-12-2019 | Vasculitis | Case Report

Look granulomatosis with polyangiitis (GPA) straight in the face: missed opportunities leading to a delayed diagnosis

Authors: N. Rolle, M. Muruganandam, I. Jan, F. M. Harji, J. Harrington, K. N. Konstantinov

Published in: Autoimmunity Highlights | Issue 1/2019

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Abstract

Granulomatosis with polyangiitis (GPA) is a systemic vasculitis with a potential to involve any organ system. It remains an important cause of kidney related morbidity and mortality. Early diagnosis can be difficult and requires high index of suspicion in all patients, but especially in cases with atypical presentation. We report a case with GPA, which was diagnosed only after new and advancing symptoms belied the original diagnosis of bilateral facial palsy and aortic mural thrombus.
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Metadata
Title
Look granulomatosis with polyangiitis (GPA) straight in the face: missed opportunities leading to a delayed diagnosis
Authors
N. Rolle
M. Muruganandam
I. Jan
F. M. Harji
J. Harrington
K. N. Konstantinov
Publication date
01-12-2019
Publisher
BioMed Central
Published in
Autoimmunity Highlights / Issue 1/2019
Print ISSN: 2038-0305
Electronic ISSN: 2038-3274
DOI
https://doi.org/10.1186/s13317-019-0118-4

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