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Published in: Japanese Journal of Radiology 5/2019

01-05-2019 | Systemic Lupus Erythematosus | Pictorial Essay

Imaging findings of mixed connective tissue disease in children and adolescents: a case series

Authors: Sureyya Burcu Gorkem, Andrea S. Doria, Shirley Tse

Published in: Japanese Journal of Radiology | Issue 5/2019

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Abstract

Mixed connective tissue disease (MCTD) is a rare disease in children and adolescents which overlaps features of juvenile idiopathic arthritis, polymyositis/dermatomyositis, systemic lupus erythematosus, and systemic sclerosis. We have provided an image-based approach for evaluation of MCTD in children and adolescents, outlying the most frequent imaging findings. This approach would aid imagers and clinicians to consider the diagnosis of this rare entity and be able to make an accurate list of differential diagnosis for complex rheumatologic diseases such as MCTD, thus facilitating the ultimate goal of early diagnosis and optimal management of affected children.
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Metadata
Title
Imaging findings of mixed connective tissue disease in children and adolescents: a case series
Authors
Sureyya Burcu Gorkem
Andrea S. Doria
Shirley Tse
Publication date
01-05-2019

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