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01-07-2019 | Ultrasound | Case Report - CSF Circulation

JEDI (jugular entrapment, dilated ventricles, intracranial hypertension) syndrome: a new clinical entity? A case report

Authors: Pasquale De Bonis, Erica Menegatti, Michele Alessandro Cavallo, Francesco Sisini, Giorgio Trapella, Alba Scerrati, Paolo Zamboni

Published in: Acta Neurochirurgica | Issue 7/2019

Abstract

Patients with idiopathic intracranial hypertension are frequently obese women with normal/slit ventricles. Patients with high-pressure hydrocephalus, instead, present enlarged ventricles. We describe a 63-year-old woman with signs and symptoms of intracranial hypertension. Brain MRI revealed hydrocephalus. Venous Doppler ultrasound showed external compression of the omohyoid muscles on the internal jugular veins. During jugular vein decompression, intracranial pressure dropped from 18 to 6 mmHg. Patient is asymptomatic at 2-year follow-up, with decreased brain ventricles. These findings could represent a novel form of high-pressure hydrocephalus that can be successfully treated without a CSF shunt. We called this syndrome JEDI (jugular entrapment dilated ventricles intracranial hypertension).

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Title: JEDI (jugular entrapment, dilated ventricles, intracranial hypertension) syndrome: a new clinical entity? A case report
Authors: Pasquale De Bonis
Erica Menegatti
Michele Alessandro Cavallo
Francesco Sisini
Giorgio Trapella
Alba Scerrati
Paolo Zamboni
Publication date: 01-07-2019
Publisher: Springer Vienna
Keywords: Ultrasound
Cranial MRI
Hydrocephalus
Hydrocephalus
Idiopathic Intracranial Hypertension
Intracranial Hypertension
Hydrocephalus
CSF Drainage
Ultrasound
Hypertension
Acetazolamide
Published in: Acta Neurochirurgica / Issue 7/2019
Print ISSN: 0001-6268
Electronic ISSN: 0942-0940
DOI: https://doi.org/10.1007/s00701-019-03908-2

2024 ASCO Annual Meeting

Springer Medicine

JEDI (jugular entrapment, dilated ventricles, intracranial hypertension) syndrome: a new clinical entity? A case report

Abstract

2024 ASCO Annual Meeting

Springer Medicine

Abstract

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