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Odontology
Published in: Odontology 2/2011

01-07-2011 | Case Report

Type III Klippel–Feil syndrome: case report and review of associated craniofacial anomalies

Authors: Venkatesh G. Naikmasur, Atul P. Sattur, R. N. Kirty, Arpita Rai Thakur

Published in: Odontology | Issue 2/2011

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Abstract

Klippel–Feil syndrome (KFS) is a complex syndrome of osseous and visceral anomalies that include the classical clinical triad of short neck, limitation of head and neck movements and low posterior hairline. It may also be associated with anomalies of the genitourinary, musculoskeletal, neurologic and cardiac systems. We report a case of type III KFS with associated rib anomalies such as cervical rib, fusion and bifid ribs, scoliosis and fused crossed renal ectopia. The aim of this paper was to summarize all craniofacial anomalies that occur in association with KFS, so that clinicians would be aware of them during diagnosis and treatment planning.
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Metadata
Title
Type III Klippel–Feil syndrome: case report and review of associated craniofacial anomalies
Authors
Venkatesh G. Naikmasur
Atul P. Sattur
R. N. Kirty
Arpita Rai Thakur
Publication date
01-07-2011
Publisher
Springer Japan
Published in
Odontology / Issue 2/2011
Print ISSN: 1618-1247
Electronic ISSN: 1618-1255
DOI
https://doi.org/10.1007/s10266-011-0004-7

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