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Journal of Interventional Cardiac Electrophysiology

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01-10-2009 | Subject of the Year

Toward early diagnosis in arrhythmogenic right ventricular dysplasia/cardiomyopathy

Author: Richard N. W. Hauer

Published in: Journal of Interventional Cardiac Electrophysiology | Issue 1/2009

Excerpt

Arrhythmogenic right ventricular dysplasia/cardiomyopathy (ARVD/C) is a myocardial disease which is histologically mainly localized in the right ventricle (RV) [1‐3]. Histology shows fibrofatty replacement of the myocardium. At autopsy, diagnosis is usually straightforward. In the clinical setting, tissue is obtained by RV endomyocardial biopsies. For safety reasons, sampling is usually carried out from the interventricular septum to avoid perforation of the affected thin RV free wall. However, histologic diagnosis by endomyocardial biopsy is hampered by (1) the often focal nature of the disease, (2) only subendocardial tissue sampling, and (3) interventricular septum rarely involved in the disease process. …

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Title: Toward early diagnosis in arrhythmogenic right ventricular dysplasia/cardiomyopathy
Author: Richard N. W. Hauer
Publication date: 01-10-2009
Publisher: Springer US
Published in: Journal of Interventional Cardiac Electrophysiology / Issue 1/2009
Print ISSN: 1383-875X
Electronic ISSN: 1572-8595
DOI: https://doi.org/10.1007/s10840-009-9420-9

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