Skip to main content
2668 search results for:

Hemophagocytic Lymphohistiocytosis 

sort by |
"newest" sorts results by publication date. "most relevant" also considers factors like how often the search phrase is in the result.
  1. 21-02-2024 | Hemophagocytic Lymphohistiocytosis | Letter

    Familial hemophagocytic lymphohistiocytosis: from macrophage activation syndrome to CLIPPERS

  2. Open Access 01-12-2024 | Campylobacter | OriginalPaper

    Hemophagocytic lymphohistiocytosis and myopericarditis induced by campylobacter: a case report

    Campylobacter spp. are gram-negative, short rods that thrive under microaerophilic conditions and do not form spores [ 1 ]. The most common sources of Campylobacter infection in humans are poultry, followed by beef and mutton [ 2 ]. Campylobacter …

  3. 01-04-2024 | Epstein-Barr Virus | OriginalPaper

    Single-Cell Transcriptomic Analysis of Epstein-Barr Virus-Associated Hemophagocytic Lymphohistiocytosis

    Epstein-Barr virus (EBV) infection can lead to infectious mononucleosis (EBV-IM) and, more rarely, EBV-associated hemophagocytic lymphohistiocytosis (EBV-HLH), which is characterized by a life-threatening hyperinflammatory cytokine storm with …

  4. 20-03-2024 | Hemophagocytic Lymphohistiocytosis | OriginalPaper

    Early hematopoietic cell transplantation for familial hemophagocytic lymphohistiocytosis in a regional treatment network in Japan

    Familial hemophagocytic lymphohistiocytosis (FHLH) is a fatal hyperinflammation syndrome arising from the genetic defect of perforin-mediated cytolysis. Curative hematopoietic cell transplantation (HCT) is needed before development of central …

  5. Open Access 01-03-2024 | Hemophagocytic Lymphohistiocytosis | OriginalPaper

    Novel Presentation of Major Histocompatibility Complex Class II Deficiency with Hemophagocytic Lymphohistiocytosis

    Major histocompatibility complex (MHC) class II deficiency is one of the autosomal recessive primary immune deficiency disorders that leads to combined immunodeficiency [ 1 ]. This mode of inheritance explains the increased frequency of this …

  6. 01-03-2024 | Hemophagocytic Lymphohistiocytosis | Letter

    Successful Treatment of Refractory EBV-Associated Hemophagocytic Lymphohistiocytosis with Combined Emapalumab and PD-1 Blockade

  7. 12-03-2024 | Visceral Leishmaniasis | OriginalPaper

    Secondary hemophagocytic lymphohistiocytosis in pediatric patients with visceral leishmaniasis and Epstein-Barr virus infection

    Visceral leishmaniasis-associated hemophagocytic lymphohistiocytosis (VL-HLH) is indistinguishable from those of HLH of other etiologies due to the overlap symptoms, posing a serious threat to life. In this study, we aimed to provide insights for …

  8. Open Access 29-03-2024 | Hemophagocytic Lymphohistiocytosis | Online First

    Differential diagnosis between kaposi sarcoma-associated herpesvirus cytokine syndrome and hemophagocytic lymphohistiocytosis

  9. 20-02-2024 | Secondary Hemophagocytic Lymphohistiocytosis | OriginalPaper

    Association of a decreased platelet count with poor survival in patients with adult secondary hemophagocytic lymphohistiocytosis

    We aimed to examine the association between baseline platelet count (PLT) and the prognosis of adult secondary hemophagocytic lymphohistiocytosis (sHLH). Data from 292 patients with pretreatment platelet counts were retrospectively analysed from …

  10. 29-02-2024 | Hemophagocytic Lymphohistiocytosis | Online First

    Hemophagocytic lymphohistiocytosis caused by herpes simplex virus type 1 in a young adult: a case report with literature review

    Hemophagocytic lymphohistiocytosis is a severe hyperinflammatory syndrome that can be potentially life-threatening without appropriate treatment. Although viral infection is the most common trigger of hemophagocytic lymphohistiocytosis, cases of …

  11. Open Access 29-12-2023 | Hemophagocytic Lymphohistiocytosis | Letter

    Refractory hemophagocytic lymphohistiocytosis secondary to polatuzumab vedotin plus rituximab and bendamustine

    Immune and antibody drug–related hemophagocytic lymphohistiocytosis (HLH) is recognized as a rare adverse event (AE) with low incidence of 0.03 to approximately 0.4% but potentially lethal, with high mortality rate of up to 50% in some cases [ 1 ].

  12. 15-02-2024 | Hemophagocytic Lymphohistiocytosis | Online First

    Flowcytometric Assessment of Activated Cytotoxic T-cells in Rapid Diagnosis of Hemophagocytic Lymphohistiocytosis in Pediatric Patients

  13. 25-12-2023 | Hemophagocytic Lymphohistiocytosis | ReviewPaper

    Liver Dysfunction in Adult Hemophagocytic Lymphohistiocytosis: A Narrative Review

    Hemophagocytic lymphohistiocytosis (HLH) is a rare, life-threatening condition that has been increasingly recognized in adults and is characterized by a hyperinflammatory state due to immune dysregulation. Its nonspecific presentation, the lack of …

  14. 26-12-2023 | Lymphoma | OriginalPaper

    Initial diagnosis of extranodal NK/T-cell lymphoma in pericardial fluid with concomitant hemophagocytic lymphohistiocytosis (HLH)

    Extranasal natural killer/T-cell lymphoma arising in the heart is rare and typically presents with non-specific clinical symptoms, necessitating a biopsy for a definitive diagnosis. We report an unusual case of a 48-year-old male who initially …

  15. Open Access 01-12-2024 | Hemophagocytic Lymphohistiocytosis | OriginalPaper

    Hemophagocytic lymphohistiocytosis following pembrolizumab and bevacizumab combination therapy for cervical cancer: a case report and systematic review

    Cancer immunotherapy using immune-checkpoint inhibitors (ICIs) has emerged as a cornerstone treatment for various cancers. However, by eliminating the physiological inhibitory control that moderates T-cell activation, ICIs may cause T-cell …

  16. Open Access 24-10-2023 | Secondary Hemophagocytic Lymphohistiocytosis | OriginalPaper

    Hemophagocytic lymphohistiocytosis—how common and how severe is it as a complication of malaria? Retrospective case series and review of the literature

    Hemophagocytic lymphohistiocytosis (HLH, formerly also named hemophagocytic syndrome) has first been described in 1939 by Scott and Robb-Smith as histiocytic medullary reticulosis [ 1 ]. Since then, the diagnosis has been subdivided into several …

  17. Open Access 10-01-2024 | Hemophagocytic Lymphohistiocytosis | OriginalPaper

    A convenient and practical index for predicting the induction response in adult patients with hemophagocytic lymphohistiocytosis: ferritin/platelet ratio

    Hemophagocytic lymphohistiocytosis (HLH) is a hyperinflammatory syndrome with high mortality rate. The response to induction therapy is an important factor affecting survival. The purpose is to investigate laboratory predictors for induction …

  18. Open Access 01-02-2024 | Human Alphaherpesvirus 3 | OriginalPaper

    Impaired STING Activation Due to a Variant in the E3 Ubiquitin Ligase AMFR in a Patient with Severe VZV Infection and Hemophagocytic Lymphohistiocytosis

    Varicella zoster virus (VZV) is a neurotropic alphaherpesvirus exclusively infecting humans, causing two distinct pathologies: varicella (chickenpox) upon primary infection and herpes zoster (shingles) following reactivation. In susceptible …

  19. Open Access 01-12-2024 | Hemophagocytic Lymphohistiocytosis | OriginalPaper

    Detection of a novel gross deletion in the UNC13D gene ends the diagnostic odyssey for a family with familial hemophagocytic lymphohistiocytosis 3

    Familial hemophagocytic lymphohistiocytosis (FHL) is an immunological disorder characterized by overactivation of macrophages and T lymphocytes. Organs, such as the liver and spleen, are affected by this uncontrolled immune response and patients …

  20. 01-12-2023 | Letter

    Severe Adenovirus Pneumonia Associated With Hemophagocytic Lymphohistiocytosis With Coronary Involvement

Filter search results

Search Operators:

„ ... ... “ Finds documents with exactly this word group, in exactly this word order and spelling (e.g., "employer branding").
AND Finds documents with both search terms (e.g., sales AND bonus).
OR Finds documents with one or the other search term (e.g., porsche OR volkswagen).
Blank Space Finds documents with all search terms. Blank space is understood as AND (e.g., man robot production).
NOT Finds documents with no appearance of the word behind NOT (e.g., ford NOT "harrison ford").
COUNT(...)>n Finds documents where the search term is mentioned at least "n" times."n" may be any number (e.g., COUNT(gear)>8).
NEAR(..., ..., ) Finds documents with both search terms in any word order, permitting "n" words as a maximum distance between them. Best choose between 15 and 30 (e.g., NEAR(recruit, professionals, 20)).
* Finds documents with the search term in word versions or composites. The star * marks whether you wish them BEFORE, BEHIND, or BEFORE and BEHIND the search term (e.g., lightweight*, *lightweight, *lightweight*).
? Finds documents with the search termn in different spellings."?" allows only one character (e.g., organi?ation).
& + - Special characters are understood as AND (e.g., Miller Bros. & Sons).

You can use operators in your search query to narrow down your results even more.

Tap the operator, or hover the mouse pointer over it, to read more about how it works.