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Open Access 19-03-2024 | Telemonitoring in Cardiology | Case Report

Wireless Pulmonary Artery Pressure Monitor Implantation in a Patient with Duchenne Muscular Dystrophy

Authors: T. Miller Sisson, Juli Sublett-Smith, Elizabeth Dupont, Russel Hirsch, Angela Lorts, Chet Villa

Abstract

Assessing heart failure progression in patients with Duchenne Muscular Dystrophy (DMD) is challenging given the multi-system nature of disease. Herein we describe the first case use of an implantable pulmonary artery pressure monitor and describe the potential clinical utility of this approach in patients with DMD.

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Dauw J, Sokolski M, Middleton JT, Nijst P, Dupont M, Forouzan O et al (2022) Ambulatory haemodynamic-guided management reduces heart failure hospitalizations in a multicentre European heart failure cohort. ESC Heart Fail 9(6):3858–3867. https://doi.org/10.1002/ehf2.14056. (Epub 3 Aug 2022)CrossRefPubMedPubMedCentral

Heywood JT, Zalawadiya S, Bourge RC, Costanzo MR, Desai AS, Rathman LD et al (2023) Sustained reduction in pulmonary artery pressures and hospitalizations during 2 years of ambulatory monitoring. J Card Fail 29(1):56–66. https://doi.org/10.1016/j.cardfail.2022.10.422. (Epub 5 Nov 2022)CrossRefPubMed

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Title: Wireless Pulmonary Artery Pressure Monitor Implantation in a Patient with Duchenne Muscular Dystrophy
Authors: T. Miller Sisson
Juli Sublett-Smith
Elizabeth Dupont
Russel Hirsch
Angela Lorts
Chet Villa
Publication date: 19-03-2024
Publisher: Springer US
Keywords: Telemonitoring in Cardiology
Duchenne Muscular Dystrophy
Neuromuscular Disorders in Children
Cardiomyopathy in Pediatrics
Heart Failure
Cardiomyopathy
Pediatric Cardiology
Published in: Pediatric Cardiology
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI: https://doi.org/10.1007/s00246-024-03459-z

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Image Credits

Implanted wireless device to monitor pulmonary artery pressure/© 2024, T. Miller Sisson et al, ACC 2024 Pediatric and Congenital Heart Disease: Year in Review/© 2024 American College of Cardiology, ACC 2024 Pulmonary Vascular Disease: Year in Review/© 2024 American College of Cardiology, ACC 2024 Valvular Heart Disease: Year in Review/© 2024 American College of Cardiology, ACC 2024 HF and Cardiomyopathies: Year in Review/© 2024 American College of Cardiology, Woman out walking/© Seventyfour / stock.adobe.com (symbolic image with model), Woman checking smartwatch /© saltdium / stock.adobe.com (symbolic image with model), Cardiac catheterization/© Damian / stock.adobe.com

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Wireless Pulmonary Artery Pressure Monitor Implantation in a Patient with Duchenne Muscular Dystrophy

Abstract

ACC 2024 Congress Coverage

Highlights from the ACC 2024 Congress

Semaglutide benefits people with type 2 diabetes and obesity-related heart failure

Incentivised to exercise

New intervention for STEMI-related cardiogenic shock

» View more highlights on the ACC 2024 congress hub page

Keynote webinar | Spotlight on sleep in brain health

Springer Medicine

Abstract

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ACC 2024 Congress Coverage

Highlights from the ACC 2024 Congress

Semaglutide benefits people with type 2 diabetes and obesity-related heart failure

Incentivised to exercise

New intervention for STEMI-related cardiogenic shock

» View more highlights on the ACC 2024 congress hub page