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Rheumatology International
Published in: Rheumatology International 3/2007

01-01-2007 | Case Report

Successful treatment of acquired amegakaryocytic thrombocytopenia with cyclosporine in adult onset Still’s disease

Authors: Min-Young Her, Tae-Hwan Kim, Hyun-Kyu Chang, Woong-Soo Lee, Dae-Hyun Yoo

Published in: Rheumatology International | Issue 3/2007

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Abstract

Acquired amegakaryocytic thrombocytopenia (AAT) is a rare disorder, characterized by severe thrombocytopenia and selective, marked decrease or absence of megakaryocytes in the bone marrow. We describe a 29-year-old female with adult onset Still’s disease preceding a diagnosis of AAT and autoimmune hemolytic anemia, which was successfully treated with cyclosporine. This is the first case of AAT in a patient with adult onset Still’s disease.
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Metadata
Title
Successful treatment of acquired amegakaryocytic thrombocytopenia with cyclosporine in adult onset Still’s disease
Authors
Min-Young Her
Tae-Hwan Kim
Hyun-Kyu Chang
Woong-Soo Lee
Dae-Hyun Yoo
Publication date
01-01-2007
Publisher
Springer-Verlag
Published in
Rheumatology International / Issue 3/2007
Print ISSN: 0172-8172
Electronic ISSN: 1437-160X
DOI
https://doi.org/10.1007/s00296-006-0202-8

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