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Indian Journal of Pediatrics

19-04-2024 | Retinoblastoma | Review Article

Management of Extraocular Retinoblastoma: ICMR Consensus Guidelines

Authors: Renu Madan, Venkatraman Radhakrishnan, Rachna Meel, Girish Chinnaswamy, Lata Singh, Suyash Kulkarni, Archana Sasi, Tanvir Kaur, Jyoti Sharma, R. S. Dhaliwal, Meena Haldorai, Gaura Kishore Rath, Sameer Bakhshi

Published in: Indian Journal of Pediatrics

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Abstract

Retinoblastoma (RB) is the most common intraocular malignancy of childhood. Advanced stage presentation of RB is common in low middle-income countries (LMICs) due to lack of awareness, social taboos associated with enucleation, seeking alternative conservative treatment options, and poor accessibility to health care. Over the last few decades, there have been significant advancements in the management of extraocular RB (EORB) which have improved outcomes and helped in minimizing treatment-related toxicities. The incorporation of multimodality approaches including chemotherapy, surgery, and radiotherapy (RT) has shown promising results; however, prognosis remains poor especially in LMICs. In this article, authors have discussed the ICMR consensus guidelines on the management of EORB, including metastatic RB.
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Metadata
Title
Management of Extraocular Retinoblastoma: ICMR Consensus Guidelines
Authors
Renu Madan
Venkatraman Radhakrishnan
Rachna Meel
Girish Chinnaswamy
Lata Singh
Suyash Kulkarni
Archana Sasi
Tanvir Kaur
Jyoti Sharma
R. S. Dhaliwal
Meena Haldorai
Gaura Kishore Rath
Sameer Bakhshi
Publication date
19-04-2024
Publisher
Springer India
Published in
Indian Journal of Pediatrics
Print ISSN: 0019-5456
Electronic ISSN: 0973-7693
DOI
https://doi.org/10.1007/s12098-024-05104-2