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World Journal of Surgical Oncology

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Open Access 01-12-2006 | Review

Pseudomyxoma peritonei – a revisit: report of 2 cases and literature review

Authors: Chunyanca Li, Rani Kanthan, SC Kanthan

Published in: World Journal of Surgical Oncology | Issue 1/2006

Abstract

Background

Pseudomyxoma peritonei (PMP) is a rare, chronic, relapsing, diagnostically challenging and poorly understood disease characterized by disseminated mucinous ascites and peritoneal implants.

Case presentation

We report two cases of PMP that represent the two biological variants of d isseminated p eritoneal a denom ucinosis (DPAM) – the benign variant and the p eritoneal m ucinous c arcinoma tosis (PMCA) – the malignant variant, both of which were characterized by multiple relapses and progression of the disease despite aggressive management.

Conclusion

Even with a better understanding and recent advances in the management of these cases, PMP remains an enigmatic disease with a protracted clinical course characterized by multiple recurrences despite surgery and/or chemotherapy. Recognition of PMP as a delayed consequence years later should alert all surgeons to be extremely vigilant when treating mucinous neoplasms of the appendix, with special care being directed towards adequate excision and thorough debridement at the initial diagnosis.

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Title: Pseudomyxoma peritonei – a revisit: report of 2 cases and literature review
Authors: Chunyanca Li
Rani Kanthan
SC Kanthan
Publication date: 01-12-2006
Publisher: BioMed Central
Published in: World Journal of Surgical Oncology / Issue 1/2006
Electronic ISSN: 1477-7819
DOI: https://doi.org/10.1186/1477-7819-4-60

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Pseudomyxoma peritonei – a revisit: report of 2 cases and literature review

Abstract

Background

Case presentation

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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