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BMC Musculoskeletal Disorders
Published in: BMC Musculoskeletal Disorders 1/2019

Open Access 01-12-2019 | Magnetic Resonance Imaging | Case report

A rare case of Gorham-stout syndrome involving the thoracic spine with progressive bilateral chylothorax: a case report

Authors: Peng Wang, Wenbo Liao, Guangru Cao, Yongyan Jiang

Published in: BMC Musculoskeletal Disorders | Issue 1/2019

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Abstract

Background

Gorham-Stout syndrome (GSS) with spinal involvement is extremely rare, and bilateral chylothorax as a complication is usually fatal. In our case, pleural effusion appeared in the left hemithorax after ligating the right thoracic duct.

Case presentation

A 14-year-old patient presented with GSS affecting the thoracic spine with bilateral chylothorax. The case was successfully managed using combined conservative and surgical treatments. At the 2-year follow-up visit, the amount of pleural fluid was reduced, the patient’s respiratory function had improved, and the deformity on the thoracic spine had gradually stabilized.

Conclusions

GSS is a rare disorder of the musculoskeletal system that responds poorly to therapies and exhibits very high morbidity and mortality. Chylothorax is a common complication when lesions involve the thoracic spine, and physicians should be vigilant for possible serious pulmonary complications.
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Metadata
Title
A rare case of Gorham-stout syndrome involving the thoracic spine with progressive bilateral chylothorax: a case report
Authors
Peng Wang
Wenbo Liao
Guangru Cao
Yongyan Jiang
Publication date
01-12-2019
Publisher
BioMed Central
Published in
BMC Musculoskeletal Disorders / Issue 1/2019
Electronic ISSN: 1471-2474
DOI
https://doi.org/10.1186/s12891-019-2542-z

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