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BMC Hematology
Published in: BMC Hematology 1/2016

Open Access 01-12-2016 | Case report

Hemophagocytic lymphohistiocytosis complicating a T-cell rich B-cell lymphoma

Authors: El Mehdi Mahtat, Maryem Zine, Mohamed Allaoui, Malika Kerbout, Nezha Messaoudi, Kamal Doghmi, Mohamed Mikdame

Published in: BMC Hematology | Issue 1/2016

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Abstract

Background

Hemophagocytic lymphohistiocytosis in adults is often secundary to an infection or a neoplasm. In this last case, T cell lymphomas are the most frequent causes. Hemophagocytic lymphohistiocytosis secundary to a B cell lymphoma has been rarely reported.

Case presentation

We describe a case of a hemophagocytic lymphohistiocytosis complicating a T-cell rich B-cell lymphoma treated with conventionnal chemotherapy leading to a complete remission.

Conclusion

Prompt etiologic diagnosis and treatment of hemophagocytic lymphohistiocytosis leads to satisfactory outcome.
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Metadata
Title
Hemophagocytic lymphohistiocytosis complicating a T-cell rich B-cell lymphoma
Authors
El Mehdi Mahtat
Maryem Zine
Mohamed Allaoui
Malika Kerbout
Nezha Messaoudi
Kamal Doghmi
Mohamed Mikdame
Publication date
01-12-2016
Publisher
BioMed Central
Published in
BMC Hematology / Issue 1/2016
Electronic ISSN: 2052-1839
DOI
https://doi.org/10.1186/s12878-016-0065-5

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