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Open Access 01-12-2014 | Case report

Perivascular epitheloid cell tumor (PEComa) mimicking retroperitoneal liposarcoma

Authors: Moritz Wildgruber, Karen Becker, Marcus Feith, Jochen Gaa

Published in: World Journal of Surgical Oncology | Issue 1/2014

Abstract

PEComas are a collection of generally rare tumors, defined by the World Health Organization as ‘mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epitheloid cells’. We describe the case of retroperitoneal PEComa with a liposarcoma-like appearance on cross-sectional imaging, but distinctive immunohistochemistry revealing the correct diagnosis.

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Title: Perivascular epitheloid cell tumor (PEComa) mimicking retroperitoneal liposarcoma
Authors: Moritz Wildgruber
Karen Becker
Marcus Feith
Jochen Gaa
Publication date: 01-12-2014
Publisher: BioMed Central
Published in: World Journal of Surgical Oncology / Issue 1/2014
Electronic ISSN: 1477-7819
DOI: https://doi.org/10.1186/1477-7819-12-3

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Perivascular epitheloid cell tumor (PEComa) mimicking retroperitoneal liposarcoma

Abstract

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