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Indian Journal of Hematology and Blood Transfusion
Published in: Indian Journal of Hematology and Blood Transfusion 1/2014

01-09-2014 | Case Report

Intraosseous Pseudotumour in a Child with Mild Hemophilia B: Report of a Rare Case and Brief Review of Literature

Authors: Radheshyam Purkait, Aritra Mukherji, Tuphan Kanti Dolai, Ramchandra Bhadra

Published in: Indian Journal of Hematology and Blood Transfusion | Special Issue 1/2014

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Abstract

Hemophilic pseudotumor is a rare, but well-known, complication of hemophilia occurring in 1–2 % of individuals with a severe factor VIII or IX deficiency. The hemophilic pseudotumor is defined as an encapsulated hematoma that increases of volume progressively by episodes of recurrent hemorrhage; usually originate in soft tissues or in subperiosteal or intraosseous areas. Very seldom, patient with mild form of hemophilia present with intraosseous pseudotumor. This report describe an 11-year-old boy with mild factor IX deficiency (17 % of normal factor IX activity), who developed a pseudotumor of the femur.
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Metadata
Title
Intraosseous Pseudotumour in a Child with Mild Hemophilia B: Report of a Rare Case and Brief Review of Literature
Authors
Radheshyam Purkait
Aritra Mukherji
Tuphan Kanti Dolai
Ramchandra Bhadra
Publication date
01-09-2014
Publisher
Springer India
Published in
Indian Journal of Hematology and Blood Transfusion / Issue Special Issue 1/2014
Print ISSN: 0971-4502
Electronic ISSN: 0974-0449
DOI
https://doi.org/10.1007/s12288-014-0414-0

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