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Open Access 01-12-2018 | Case Report

A Case of Concomitant Pemphigus Foliaceus and Oral Pemphigus Vulgaris

Authors: Alexandra C. Perks, Paula M. Farthing, Ruth Murphy, Anne M. Hegarty

Published in: Head and Neck Pathology | Issue 4/2018

Abstract

Pemphigus is a chronic autoimmune condition that can affect multiple areas of the body. The two main subtypes of pemphigus are pemphigus vulgaris (PV) and pemphigus foliaceus (PF) which can rarely occur concurrently or even transition from one to the other. The process of transition may be explained by qualitative changes in desmoglein autoantibody profile. We present a rare case of concomitant PF and oral PV and explore the literature on transitions between pemphigus subtypes and whether this case could represent a transition from PF to PV. Furthermore, the realities of multidisciplinary patient management are discussed.

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Title: A Case of Concomitant Pemphigus Foliaceus and Oral Pemphigus Vulgaris
Authors: Alexandra C. Perks
Paula M. Farthing
Ruth Murphy
Anne M. Hegarty
Publication date: 01-12-2018
Publisher: Springer US
Published in: Head and Neck Pathology / Issue 4/2018
Electronic ISSN: 1936-0568
DOI: https://doi.org/10.1007/s12105-017-0884-0

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A Case of Concomitant Pemphigus Foliaceus and Oral Pemphigus Vulgaris

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