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Published in: Journal of Gastrointestinal Cancer 4/2011

01-12-2011 | Case Report

Nested Stromal Epithelial Tumor of the Liver—Liver Transplantation and Follow-Up

Authors: Merten Hommann, Daniel Kaemmerer, Wolfgang Daffner, Vikas Prasad, Richard Paul Baum, Alexander Petrovitch, Axel Sauerbrey, Katrin Katenkamp, Roland Kaufmann, Utz Settmacher

Published in: Journal of Gastrointestinal Cancer | Issue 4/2011

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Abstract

Background

The nested stromal epithelial tumor (NSET) of the liver is a rare tumor entity which is being reported in young girls.

Case Report

In our 16-year-old female patient, we have performed a liver transplantation (LTX) for a non-metastasizing non-resectable liver tumor. The patient was tumor free in the follow-up. At 28 months postoperatively, we detected lung metastases in the F18-FDG-PET/CT. The patient died 37 months after LTX from progressive pulmonary metastases.

Conclusion

LTX should not have been generally recommended for NSET. Further statements about the value of LTX for NSET will be possible only after evaluation of the course of the disease in a larger number of transplanted patients.
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Metadata
Title
Nested Stromal Epithelial Tumor of the Liver—Liver Transplantation and Follow-Up
Authors
Merten Hommann
Daniel Kaemmerer
Wolfgang Daffner
Vikas Prasad
Richard Paul Baum
Alexander Petrovitch
Axel Sauerbrey
Katrin Katenkamp
Roland Kaufmann
Utz Settmacher
Publication date
01-12-2011
Publisher
Springer US
Published in
Journal of Gastrointestinal Cancer / Issue 4/2011
Print ISSN: 1941-6628
Electronic ISSN: 1941-6636
DOI
https://doi.org/10.1007/s12029-010-9248-7

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