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Journal of Clinical Immunology

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01-10-2021 | Neutrophilic Dermatosis | Letter to Editor

A Case of VEXAS Syndrome Complicated by Hemophagocytic Lymphohistiocytosis

Authors: Alice Grey, Pak Leng Cheong, Frederick J. Lee, Edward Abadir, James Favaloro, Shihong Yang, Stephen Adelstein

Published in: Journal of Clinical Immunology | Issue 7/2021

Excerpt

To the Editors, …

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Charbonneau ME, Passalacqua KD, Hagen SE, et al. Perturbation of ubiquitin homeostasis promotes macrophage oxidative defenses. Sci Rep. 2019; 9(1):10245. https://doi.org/10.1038/s41598-019-46526-9.

Egues Dubuc CA, et al. THU0452 secondary hemophagocytic lymphohistiocytosis: a series of 11 patients. Literature review. Ann Rheum Dis. 2013;72(Suppl 3):A317–A317.CrossRef

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Lee SMS, Fan BE, Lim JH, Goh LL, Lee JSS, Koh LW. A case of VEXAS syndrome manifesting as Kikuchi-Fujimoto disease, relapsing polychondritis, venous thromboembolism and macrocytic anaemia. Rheumatology (Oxford). 2021. https://doi.org/10.1093/rheumatology/keab200.

Magnol M, Couvaras L, Degboé Y, Delabesse E, Bulai-Livideanu C, Ruyssen-Witrand A, et al. VEXAS syndrome in a patient with previous spondyloarthritis with a favourable response to intravenous immunoglobulin and anti-IL17 therapy. Rheumatology. 2021. https://doi.org/10.1093/rheumatology/keab211.

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Title: A Case of VEXAS Syndrome Complicated by Hemophagocytic Lymphohistiocytosis
Authors: Alice Grey
Pak Leng Cheong
Frederick J. Lee
Edward Abadir
James Favaloro
Shihong Yang
Stephen Adelstein
Publication date: 01-10-2021
Publisher: Springer US
Keywords: Neutrophilic Dermatosis
Hemophagocytic Lymphohistiocytosis
Hemophagocytic Lymphohistiocytosis
VEXAS Syndrome
Published in: Journal of Clinical Immunology / Issue 7/2021
Print ISSN: 0271-9142
Electronic ISSN: 1573-2592
DOI: https://doi.org/10.1007/s10875-021-01070-y

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