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01-07-2013 | Astute Clinician Report

Hypocomplementemic Urticarial Vasculitis (HUVS) with Precocious Emphysema Responsive to Azathioprine

Authors: L. Breda, M. Nozzi, S. Harari, M Del Torto, M. Lucantoni, A. Scardapane, F. Chiarelli

Published in: Journal of Clinical Immunology | Issue 5/2013

Excerpt

Hypocomplementemic urticarial vasculitis syndrome (HUVS) is an uncommon small-vessel vasculitis first described by McDuffie and colleagues in 1973 [1]. Diagnostic criteria proposed by the same authors include two major criteria (urticaria lasting more than 6 months, hypocomplementemia) plus two minor criteria (leukocytoclastic vasculitis, arthralgia or arthritis, uveitis or episcleritis, glomerulonephritis, recurrent abdominal pain, positive C1 q precipitin test result) [2]. …

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Title: Hypocomplementemic Urticarial Vasculitis (HUVS) with Precocious Emphysema Responsive to Azathioprine
Authors: L. Breda
M. Nozzi
S. Harari
M Del Torto
M. Lucantoni
A. Scardapane
F. Chiarelli
Publication date: 01-07-2013
Publisher: Springer US
Published in: Journal of Clinical Immunology / Issue 5/2013
Print ISSN: 0271-9142
Electronic ISSN: 1573-2592
DOI: https://doi.org/10.1007/s10875-013-9886-1

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