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01-08-2016 | Clinical Report

Emergency bronchoscopy for foreign-body aspiration in a child with type I mucopolysaccharidosis: a challenging airway management experience

Authors: Pinar Kendigelen, Yusuf Tunali, Ayse Tutuncu, Gulruh Ashyralyyeva, Senol Emre, Guner Kaya

Published in: Journal of Anesthesia | Issue 4/2016

Abstract

The mucopolysaccharidosis (MPS) is a rare lysosomal storage disease. Glycosaminoglycans (GAG) accumulate in musculoskeletal system, connective tissues. Enlarged tongue, short immobile neck, and limited mobility of the cervical spine and temporomandibular joints render the airway management potentially risky. MPS children have high anesthetic risks, especially in airway management of emergency situations. The foreign-body aspiration requiring intervention with rigid bronchoscopy is an urgent and risky clinical situation. We present our experience with a challenging airway management with a three-year-old child with MPS who needed emergency bronchoscopy due to peanut aspiration.

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Title: Emergency bronchoscopy for foreign-body aspiration in a child with type I mucopolysaccharidosis: a challenging airway management experience
Authors: Pinar Kendigelen
Yusuf Tunali
Ayse Tutuncu
Gulruh Ashyralyyeva
Senol Emre
Guner Kaya
Publication date: 01-08-2016
Publisher: Springer Japan
Published in: Journal of Anesthesia / Issue 4/2016
Print ISSN: 0913-8668
Electronic ISSN: 1438-8359
DOI: https://doi.org/10.1007/s00540-016-2180-7

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Emergency bronchoscopy for foreign-body aspiration in a child with type I mucopolysaccharidosis: a challenging airway management experience

Abstract

Keynote webinar | Spotlight on sleep in brain health

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Abstract

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