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01-12-2020 | Patent Ductus Arteriosus | Case Report

Prenatal Diagnosis of Isolated Atrioventricular Discordance and Ventriculoarterial Concordance and Double-Outlet Right Ventricle in Situs Inversus: Case Report and Review of the Literature

Authors: Saif Aljemmali, John Bokowski, Karim Diab

Published in: Pediatric Cardiology | Issue 8/2020

Abstract

Atrioventricular (AV) discordance and ventriculoarterial (VA) concordance in the setting of visceral situs inversus are one of the rarest forms of cardiac malformations. To our knowledge, this is the first reported case of prenatal diagnosis of such rare cardiac anatomy in association with double-outlet right ventricle on fetal echocardiography. The physiology of this cardiac anomaly is similar to that of transposition of the great arteries, and the best surgical option is the atrial switch operation.

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Title: Prenatal Diagnosis of Isolated Atrioventricular Discordance and Ventriculoarterial Concordance and Double-Outlet Right Ventricle in Situs Inversus: Case Report and Review of the Literature
Authors: Saif Aljemmali
John Bokowski
Karim Diab
Publication date: 01-12-2020
Publisher: Springer US
Keywords: Patent Ductus Arteriosus
Patent Ductus Arteriosus
Echocardiography
Patent Ductus Arteriosus
Ventricular Septal Defect
Patent Ductus Arteriosus
Echocardiography
Transposition of the Great Artery
Ventricular Septal Defect
Published in: Pediatric Cardiology / Issue 8/2020
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI: https://doi.org/10.1007/s00246-020-02467-z

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