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Published in: Endocrine 2/2019

Open Access 01-11-2019 | Pituitary Adenoma | Review

Treatment challenges in pediatric Cushing’s disease: Review of the literature with particular emphasis on predictive factors for the disease recurrence

Authors: Katarzyna Pasternak-Pietrzak, Elżbieta Moszczyńska, Mieczysław Szalecki

Published in: Endocrine | Issue 2/2019

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Abstract

Cushing’s disease (CD) is a rare endocrine condition caused by a corticotroph pituitary tumor that produces adrenocorticotropic hormone. The current state of knowledge of CD treatment is presented in this article including factors that can be helpful in predicting remission and/or recurrence of the disease. The primary goals in CD treatment are quick diagnosis and effective, prompt treatment as the persistent disease is associated with increased morbidity and mortality. Cooperation of a team consisting of experienced pediatrician/adult endocrinologist, neuroradiologist, transsphenoidal neurosurgeon and (if necessary) radiotherapist contribute to the best treatment effects.
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Metadata
Title
Treatment challenges in pediatric Cushing’s disease: Review of the literature with particular emphasis on predictive factors for the disease recurrence
Authors
Katarzyna Pasternak-Pietrzak
Elżbieta Moszczyńska
Mieczysław Szalecki
Publication date
01-11-2019
Publisher
Springer US
Published in
Endocrine / Issue 2/2019
Print ISSN: 1355-008X
Electronic ISSN: 1559-0100
DOI
https://doi.org/10.1007/s12020-019-02036-2

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