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Published in: Current Allergy and Asthma Reports 9/2020

01-09-2020 | Vasculitis | Autoimmunity (T Tarrant, Section Editor)

Cogan’s Syndrome: Clinical Presentations and Update on Treatment

Authors: Gabriela Mabel Espinoza, Joseph Wheeler, Katherine K. Temprano, Angela Prost Keller

Published in: Current Allergy and Asthma Reports | Issue 9/2020

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Abstract

Purpose of Review

Cogan’s syndrome (CS) is a rare systemic vasculitis that can severely affect vision and hearing, which may also have significant systemic effects. Early recognition of this autoimmune disorder and intervention can minimize disabling and irreversible damage.

Recent Findings

This article will review the varying clinical presentations of CS and emerging information of systemic disease associated with CS. We will also review recently published promising treatment outcomes using immune modulating medications.

Summary

As our framework for recognizing the markers of CS and the associated systemic disorders expands, more effective guidelines and treatment options may emerge.
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Metadata
Title
Cogan’s Syndrome: Clinical Presentations and Update on Treatment
Authors
Gabriela Mabel Espinoza
Joseph Wheeler
Katherine K. Temprano
Angela Prost Keller
Publication date
01-09-2020
Publisher
Springer US
Published in
Current Allergy and Asthma Reports / Issue 9/2020
Print ISSN: 1529-7322
Electronic ISSN: 1534-6315
DOI
https://doi.org/10.1007/s11882-020-00945-1

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