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Open Access 01-12-2008 | Case report

Intravascular leiomyosarcoma of the brachiocephalic region – report of an unusual tumour localisation: case report and review of the literature

Authors: Daniel-Johannes Tilkorn, Marcus Lehnhardt, Jörg Hauser, Adrien Daigeler, Detlev Hebebrand, Thomas Mentzel, Hans Ulrich Steinau, Cornelius Kuhnen

Published in: World Journal of Surgical Oncology | Issue 1/2008

Abstract

Background

Intravascular leiomyosarcoma is a rare tumour entity originating from venous vessel structures and most frequently affecting the inferior vena cava.

Case presentation

A 69-year old patient presented with a biopsy proven leiomyosarcoma of the right supraclavicular region. Tumour resection and histological assessment verified the intravascular tumour origin arising from the internal jugular vein and extending into the surrounding soft tissue.

Conclusion

In the presence of a biopsy proven diagnosis of leiomyosarcoma the rare condition of an intravascular tumour origin has to be considered even without signs of venous stases. This may result in an altered surgical strategy. Microthrombembolism and pulmonary metastases may complicate the course of the disease.

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Title: Intravascular leiomyosarcoma of the brachiocephalic region – report of an unusual tumour localisation: case report and review of the literature
Authors: Daniel-Johannes Tilkorn
Marcus Lehnhardt
Jörg Hauser
Adrien Daigeler
Detlev Hebebrand
Thomas Mentzel
Hans Ulrich Steinau
Cornelius Kuhnen
Publication date: 01-12-2008
Publisher: BioMed Central
Published in: World Journal of Surgical Oncology / Issue 1/2008
Electronic ISSN: 1477-7819
DOI: https://doi.org/10.1186/1477-7819-6-113

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Intravascular leiomyosarcoma of the brachiocephalic region – report of an unusual tumour localisation: case report and review of the literature

Abstract

Background

Case presentation

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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