Issue 1/2011
Content (10 Articles)
Tau, prions and Aβ: the triad of neurodegeneration
Lilla Reiniger, Ana Lukic, Jacqueline Linehan, Peter Rudge, John Collinge, Simon Mead, Sebastian Brandner
Genetic Creutzfeldt–Jakob disease and fatal familial insomnia: insights into phenotypic variability and disease pathogenesis
Sabina Capellari, Rosaria Strammiello, Daniela Saverioni, Hans Kretzschmar, Piero Parchi
Genetic Creutzfeldt-Jakob disease associated with the E200K mutation: characterization of a complex proteinopathy
Gabor G. Kovacs, Jérémie Seguin, Isabelle Quadrio, Romana Höftberger, István Kapás, Nathalie Streichenberger, Anne Gaëlle Biacabe, David Meyronet, Raf Sciot, Rik Vandenberghe, Katalin Majtenyi, Lajos László, Thomas Ströbel, Herbert Budka, Armand Perret-Liaudet
A novel seven-octapeptide repeat insertion in the prion protein gene (PRNP) in a Dutch pedigree with Gerstmann–Sträussler–Scheinker disease phenotype: comparison with similar cases from the literature
Casper Jansen, Willem Voet, Mark W. Head, Piero Parchi, Helen Yull, Aad Verrips, Pieter Wesseling, Jan Meulstee, Frank Baas, Willem A. van Gool, James W. Ironside, Annemieke J. M. Rozemuller
Molecular pathology of human prion disease
Jonathan D. F. Wadsworth, John Collinge
Molecular biology and pathology of prion strains in sporadic human prion diseases
Pierluigi Gambetti, Ignazio Cali, Silvio Notari, Qingzhong Kong, Wen-Quan Zou, Witold K. Surewicz
Phenotypic variability of sporadic human prion disease and its molecular basis: past, present, and future
Piero Parchi, Rosaria Strammiello, Armin Giese, Hans Kretzschmar
Cellular and sub-cellular pathology of animal prion diseases: relationship between morphological changes, accumulation of abnormal prion protein and clinical disease
Martin Jeffrey, Gillian McGovern, Silvia Sisó, Lorenzo González
The application of in vitro cell-free conversion systems to human prion diseases
Michael Jones, Alexander H. Peden, Mark W. Head, James W. Ironside