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Open Access 01-12-2013 | Case report

Video-assisted thoracoscopic surgery for recurrent pneumothorax in pulmonary lymphangioleimyomatosis with tuberous sclerosis complex

Authors: Chia-Fen Tsai, Chen-Hao Hsiao, Jang-Ming Lee, Ke-Cheng Chen, Ming-Jium Shieh, Hong-Shiee Lai, Jin-Shing Chen

Published in: Journal of Cardiothoracic Surgery | Issue 1/2013

Abstract

Pneumothorax in pulmonary lymphangioleiomyomatosis (LAM) with tuberous sclerosis complex (TSC) is a difficult condition to manage. Video-assisted thoracoscopic surgery (VATS) may play a role in diagnosis and treatment of this situation. We present a case of right recurrent pneumothorax due to LAM with TSC in whom VATS was performed for pathological diagnosis and mechanical pleurodesis. The unique presentation of LAM in TSC was also discussed.

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Title: Video-assisted thoracoscopic surgery for recurrent pneumothorax in pulmonary lymphangioleimyomatosis with tuberous sclerosis complex
Authors: Chia-Fen Tsai
Chen-Hao Hsiao
Jang-Ming Lee
Ke-Cheng Chen
Ming-Jium Shieh
Hong-Shiee Lai
Jin-Shing Chen
Publication date: 01-12-2013
Publisher: BioMed Central
Published in: Journal of Cardiothoracic Surgery / Issue 1/2013
Electronic ISSN: 1749-8090
DOI: https://doi.org/10.1186/1749-8090-8-101

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Video-assisted thoracoscopic surgery for recurrent pneumothorax in pulmonary lymphangioleimyomatosis with tuberous sclerosis complex

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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