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The Cerebellum
Published in: The Cerebellum 6/2019

01-12-2019 | Vestibulopathy | Review

Deafness and Vestibulopathy in Cerebellar Diseases: a Practical Approach

Authors: Orlando G. Barsottini, José Luiz Pedroso, Carlos Roberto Martins Jr, Marcondes Cavalcante França Jr, Pedro Mangabeira Albernaz

Published in: The Cerebellum | Issue 6/2019

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Abstract

Cerebellar ataxias are a clinically heterogeneous group of neurological disorders. Besides the cerebellum, several forms of hereditary ataxias or non-genetic ataxias also affect other areas of the brain. Some forms of cerebellar ataxias may have cochlear and vestibular involvement and may present with deafness and symptoms or signs of vestibulopathy (dizziness, nystagmus and diplopia). Recognizing otoneurological symptoms in patients with cerebellar ataxias is mandatory, since these signs may guide a specific diagnosis, and clinicians may provide a suitable therapeutic approach. In this review, we describe and discuss the most common forms of cerebellar ataxias associated with deafness and vestibulopathy.
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Metadata
Title
Deafness and Vestibulopathy in Cerebellar Diseases: a Practical Approach
Authors
Orlando G. Barsottini
José Luiz Pedroso
Carlos Roberto Martins Jr
Marcondes Cavalcante França Jr
Pedro Mangabeira Albernaz
Publication date
01-12-2019
Publisher
Springer US
Published in
The Cerebellum / Issue 6/2019
Print ISSN: 1473-4222
Electronic ISSN: 1473-4230
DOI
https://doi.org/10.1007/s12311-019-01042-4

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