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Documenta Ophthalmologica

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01-12-2019 | Vasculitis | Clinical Case Report

Novel findings in enhanced S-cone syndrome: a case with macular retinal neovascularization and severe retinal vasculitis

Authors: Fatemeh Bazvand, Hasan Khojasteh, Mohammad Zarei

Published in: Documenta Ophthalmologica | Issue 3/2019

Abstract

Purpose

To describe a novel association of enhanced S-cone syndrome (ESCS) with macular retinal neovascularization and severe retinal vasculitis.

Methods

Clinical examination, spectral domain optical coherence tomography, fluorescein angiography, fundus autofluorescence, infrared reflectance and electroretinography were used to study a 25-year-old male with a history of night blindness from early childhood and recent accelerated visual loss in right eye.

Results

Pigmented lesions were observed along the arcades without peripheral retinal involvement. Intraretinal cystoid spaces, retinal neovascularization of posterior pole and severe peripheral and posterior retinal vasculitis were found on clinical examination and multimodal imaging. Based on characteristic clinical and electroretinographic findings, a diagnosis of ESCS was made.

Conclusion

This case highlights novel associations of retinal neovascularization and vasculitis with ESCS.

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Title: Novel findings in enhanced S-cone syndrome: a case with macular retinal neovascularization and severe retinal vasculitis
Authors: Fatemeh Bazvand
Hasan Khojasteh
Mohammad Zarei
Publication date: 01-12-2019
Publisher: Springer Berlin Heidelberg
Keywords: Vasculitis
Vasculitis
Night-Blindness
Pigmentary Retinopathy
Published in: Documenta Ophthalmologica / Issue 3/2019
Print ISSN: 0012-4486
Electronic ISSN: 1573-2622
DOI: https://doi.org/10.1007/s10633-019-09706-6

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Springer Medicine

Novel findings in enhanced S-cone syndrome: a case with macular retinal neovascularization and severe retinal vasculitis

Abstract

Purpose

Methods

Results

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Purpose

Methods

Results

Conclusion

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