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Published in: CEN Case Reports 1/2015

01-05-2015 | Case Report

Uterus didelphys with obstructed hemivagina and contralateral multicystic dysplastic kidney

Authors: Masaki Shimizu, Seisho Sakai, Kazuhide Ohta, Masatoshi Miyamoto, Akihiro Yachie

Published in: CEN Case Reports | Issue 1/2015

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Abstract

Müllerian anomalies are often associated with urinary tract anomalies. Herlyn–Werner–Wunderlich syndrome or obstructed hemivagina and ipsilateral renal anomaly are rare Müllerian anomaly comprising uterine didelphys, obstructed hemivagina, and ipsilateral renal anomaly. We report an unusual case of uterus didelphys with obstructed hemivagina and contralateral (not ipsilateral) multicystic dysplastic kidney. An early diagnosis is critical to prevent complications such as adhesions with subsequent infertility. A careful evaluation of the female reproductive tract may be necessary in children with not only renal aplasia but also lateral renal anomalies such as multicystic dysplastic kidney.
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Metadata
Title
Uterus didelphys with obstructed hemivagina and contralateral multicystic dysplastic kidney
Authors
Masaki Shimizu
Seisho Sakai
Kazuhide Ohta
Masatoshi Miyamoto
Akihiro Yachie
Publication date
01-05-2015
Publisher
Springer Japan
Published in
CEN Case Reports / Issue 1/2015
Electronic ISSN: 2192-4449
DOI
https://doi.org/10.1007/s13730-014-0139-9

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