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World Journal of Surgical Oncology

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Open Access 01-12-2012 | Case report

Primitive neuroectodermal tumor of the kidney: case report and review of literature

Authors: Chuanyu Sun, Zunguo Du, Shijun Tong, Ke Xu, Weihong Ding, Jianliang Sun, Qiang Ding

Published in: World Journal of Surgical Oncology | Issue 1/2012

Abstract

Background

Renal primitive neuroectodermal tumor (rPNET) as a member of Ewing’s sarcoma family is extremely rare and usually occurs in children and young adults. Most literature about rPNET was isolated case reports.

Case presentation

We reported a case of 45-year-old man with the complaint of right flank pain. Computerized tomography (CT) scan demonstrated a large substantive tumor involving the lower pole of the right kidney. Then the patient underwent radical nephrectomy. Pathologic characteristics and immunohistochemical analysis confirmed the diagnosis of rPNET. Additionally, the patient received three cycles of chemotherapy, and was still alive without metastasis at 15-months follow-up.

Conclusion

rPNET is rare and presents aggressive clinical behavior and worse prognosis. We expect that further awareness and study of this rare tumor can be had by presenting our case.

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Title: Primitive neuroectodermal tumor of the kidney: case report and review of literature
Authors: Chuanyu Sun
Zunguo Du
Shijun Tong
Ke Xu
Weihong Ding
Jianliang Sun
Qiang Ding
Publication date: 01-12-2012
Publisher: BioMed Central
Published in: World Journal of Surgical Oncology / Issue 1/2012
Electronic ISSN: 1477-7819
DOI: https://doi.org/10.1186/1477-7819-10-279

At a glance: The STEP trials

Springer Medicine

Primitive neuroectodermal tumor of the kidney: case report and review of literature

Abstract

Background

Case presentation

Conclusion

At a glance: The STEP trials

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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