Skip to main content
Top
Published in: Digestive Diseases and Sciences 1/2019

01-01-2019 | Stanford Multidisciplinary Seminars

The Runs: Sudden Copious Ostomy Output in an Acolonic Hirschsprung Disease Patient with Short Gut Syndrome

Authors: Warapan Nakayuenyongsuk, Danielle Barnes, Brock Martin, Megan Christofferson, John Kerner

Published in: Digestive Diseases and Sciences | Issue 1/2019

Login to get access

Excerpt

A 7-year-old female with prior history of total colonic and ileal Hirschsprung disease was initially evaluated for very high ostomy output of unknown etiology. Her medical history had included extensive surgical interventions prior to 2 years of age to resect involved bowel. Those resections resulted in short gut (residual length of small bowel 145 cm), an end jejunostomy, and the absence of an ileocecal valve or colon. During those first 2 years, due in part to dilated proximal small bowel, she underwent three Serial Transverse Enteroplasty (STEP) procedures in order to lengthen and taper (narrow) her intestine [1, 2]. …
Literature
1.
go back to reference Kim HB, Lee PW, Garza J, et al. Serial transverse enteroplasty for short bowel syndrome: a case report. J Pediatr Surg. 2003;38:881–885.CrossRef Kim HB, Lee PW, Garza J, et al. Serial transverse enteroplasty for short bowel syndrome: a case report. J Pediatr Surg. 2003;38:881–885.CrossRef
2.
go back to reference Abu-Elmagd K. The concept of gut rehabilitation and the future of visceral transplantation. Nat RevGastroenterol Hepatol. 2015;12:108–120.CrossRef Abu-Elmagd K. The concept of gut rehabilitation and the future of visceral transplantation. Nat RevGastroenterol Hepatol. 2015;12:108–120.CrossRef
3.
go back to reference Cohran VC, Prozialeck JD, Cole CR. Redefining Short Bowel Syndrome in the 21st Century. Pediatric Research. 2017: Advance online publication 25 January 2017. Cohran VC, Prozialeck JD, Cole CR. Redefining Short Bowel Syndrome in the 21st Century. Pediatric Research. 2017: Advance online publication 25 January 2017.
4.
go back to reference Barker J, Liu E. Celiac disease: pathophysiology, clinical manifestations and associated autoimmune conditions. Adv Pediatr. 2008;55:349–365.CrossRef Barker J, Liu E. Celiac disease: pathophysiology, clinical manifestations and associated autoimmune conditions. Adv Pediatr. 2008;55:349–365.CrossRef
5.
go back to reference West J, Fleming K, Tata L, et al. Incidence and prevalence of celiac disease and dermatitis herpetiformis in the UK over two decades: population-based study. Am J Gastroenterol. 2014;109:757–768.CrossRef West J, Fleming K, Tata L, et al. Incidence and prevalence of celiac disease and dermatitis herpetiformis in the UK over two decades: population-based study. Am J Gastroenterol. 2014;109:757–768.CrossRef
7.
go back to reference Hill ID, Fasano A, Guandalini S, et al. NASPGHAN clinical report on the diagnosis and treatment of gluten related disorders. J Pediatr Gastroenterol Nutr. 2016;63:156–165.CrossRef Hill ID, Fasano A, Guandalini S, et al. NASPGHAN clinical report on the diagnosis and treatment of gluten related disorders. J Pediatr Gastroenterol Nutr. 2016;63:156–165.CrossRef
8.
go back to reference Hill ID, Dirks MH, Liptak GS, et al. Guideline for the diagnosis and treatment of celiac disease in children: recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition. J Pediatr Gastroenterol Nutr. 2005;40:1–19.CrossRef Hill ID, Dirks MH, Liptak GS, et al. Guideline for the diagnosis and treatment of celiac disease in children: recommendations of the North American Society for Pediatric Gastroenterology, Hepatology and Nutrition. J Pediatr Gastroenterol Nutr. 2005;40:1–19.CrossRef
9.
go back to reference Husby S, Koletzko S, Korponay-Szabo IR, et al. European society for pediatric gastroenterology hepatology, and nutrition guidelines for the diagnosis of coeliac disease. J Pediatr Gastroenterol Nutr. 2012;54:136–160.CrossRef Husby S, Koletzko S, Korponay-Szabo IR, et al. European society for pediatric gastroenterology hepatology, and nutrition guidelines for the diagnosis of coeliac disease. J Pediatr Gastroenterol Nutr. 2012;54:136–160.CrossRef
Metadata
Title
The Runs: Sudden Copious Ostomy Output in an Acolonic Hirschsprung Disease Patient with Short Gut Syndrome
Authors
Warapan Nakayuenyongsuk
Danielle Barnes
Brock Martin
Megan Christofferson
John Kerner
Publication date
01-01-2019
Publisher
Springer US
Published in
Digestive Diseases and Sciences / Issue 1/2019
Print ISSN: 0163-2116
Electronic ISSN: 1573-2568
DOI
https://doi.org/10.1007/s10620-018-5229-7

Other articles of this Issue 1/2019

Digestive Diseases and Sciences 1/2019 Go to the issue
Live Webinar | 27-06-2024 | 18:00 (CEST)

Keynote webinar | Spotlight on medication adherence

Live: Thursday 27th June 2024, 18:00-19:30 (CEST)

WHO estimates that half of all patients worldwide are non-adherent to their prescribed medication. The consequences of poor adherence can be catastrophic, on both the individual and population level.

Join our expert panel to discover why you need to understand the drivers of non-adherence in your patients, and how you can optimize medication adherence in your clinics to drastically improve patient outcomes.

Prof. Kevin Dolgin
Prof. Florian Limbourg
Prof. Anoop Chauhan
Developed by: Springer Medicine
Obesity Clinical Trial Summary

At a glance: The STEP trials

A round-up of the STEP phase 3 clinical trials evaluating semaglutide for weight loss in people with overweight or obesity.

Developed by: Springer Medicine

Highlights from the ACC 2024 Congress

Year in Review: Pediatric cardiology

Watch Dr. Anne Marie Valente present the last year's highlights in pediatric and congenital heart disease in the official ACC.24 Year in Review session.

Year in Review: Pulmonary vascular disease

The last year's highlights in pulmonary vascular disease are presented by Dr. Jane Leopold in this official video from ACC.24.

Year in Review: Valvular heart disease

Watch Prof. William Zoghbi present the last year's highlights in valvular heart disease from the official ACC.24 Year in Review session.

Year in Review: Heart failure and cardiomyopathies

Watch this official video from ACC.24. Dr. Biykem Bozkurt discusses last year's major advances in heart failure and cardiomyopathies.