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Pediatric Radiology

14-05-2024 | Osteomyelitis | Pictorial Essay

The many faces of sickle cell disease in children: complications in the appendicular skeleton

Authors: Marcela De La Hoz Polo, Victoria E. Hudson, John Adu, Subarna Chakravorty, Saira Haque

Published in: Pediatric Radiology

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Abstract

Sickle cell disease (SCD) is a hereditary red cell disorder with clinical manifestations secondary to sickling or crescent-shaped distortion of the red blood cells. Musculoskeletal complications of SCD are often the main causes for acute and chronic morbidities in children with manifestations including osteomyelitis, osteoporosis and osteonecrosis. This article aims to familiarise the paediatric radiologist with appendicular skeletal complications of SCD in the paediatric population and their imaging appearance.
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Metadata
Title
The many faces of sickle cell disease in children: complications in the appendicular skeleton
Authors
Marcela De La Hoz Polo
Victoria E. Hudson
John Adu
Subarna Chakravorty
Saira Haque
Publication date
14-05-2024
Publisher
Springer Berlin Heidelberg
Published in
Pediatric Radiology
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI
https://doi.org/10.1007/s00247-024-05913-9