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Pediatric Rheumatology

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Open Access 01-12-2019 | Systemic Lupus Erythematosus | Case Report

Juvenile systemic lupus erythematosus presenting as pancarditis

Authors: D. O’Leary, C. O’Connor, L. Nertney, E. J. MacDermott, D. Mullane, O. Franklin, O. G. Killeen

Published in: Pediatric Rheumatology | Issue 1/2019

Abstract

Background

Systemic lupus erythematosus (SLE) is a chronic autoimmune disease with marked variation in its clinical presentation. Juvenile SLE (jSLE) accounts for 15–20% of all cases and is diagnosed when SLE manifests before 18 years of age. Pancarditis is a rare complication of SLE, regardless of age of disease onset.

Case presentation

We report a case of jSLE in a 15 year old Caucasian female presenting with an acute episode of pancarditis and multiorgan dysfunction who was successfully treated with systemic corticosteroids and cyclophosphamide.

Conclusion

Pancarditis can be a presenting feature of jSLE which was previously unreported. A high index of suspicion for severe cardiac involvement is required at all stages of disease.

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Title: Juvenile systemic lupus erythematosus presenting as pancarditis
Authors: D. O’Leary
C. O’Connor
L. Nertney
E. J. MacDermott
D. Mullane
O. Franklin
O. G. Killeen
Publication date: 01-12-2019
Publisher: BioMed Central
Keywords: Systemic Lupus Erythematosus
Echocardiography
Pancarditis
Echocardiography
Published in: Pediatric Rheumatology / Issue 1/2019
Electronic ISSN: 1546-0096
DOI: https://doi.org/10.1186/s12969-019-0372-z

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Juvenile systemic lupus erythematosus presenting as pancarditis

Abstract

Background

Case presentation

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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