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BMC Gastroenterology
Published in: BMC Gastroenterology 1/2015

Open Access 01-12-2015 | Case report

Synchronous mucosal Schwann-cell hamartomas in a young adult suggestive of mucosal Schwann-cell harmatomatosis: a case report

Authors: Jeong Mo Bae, Joon Young Lee, Junhun Cho, Sang Ah Lim, Gyeong Hoon Kang

Published in: BMC Gastroenterology | Issue 1/2015

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Abstract

Background

Mucosal Schwann-cell hamartoma is a rare mesenchymal polyp that presents in the intestine. Despite lacking ganglion cells, it resembles a gastrointestinal ganglioneuroma.

Case presentation

We report a case of synchronous mucosal Schwann-cell hamartomas in a young male patient, who presented with a single discrete polyp in the mid-rectum and multiple polypoid mucosal lesions in the distal rectum.

Conclusion

To the best of our knowledge, this is the first report of a case of multiple mucosal Schwann-cell hamartomas.
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Metadata
Title
Synchronous mucosal Schwann-cell hamartomas in a young adult suggestive of mucosal Schwann-cell harmatomatosis: a case report
Authors
Jeong Mo Bae
Joon Young Lee
Junhun Cho
Sang Ah Lim
Gyeong Hoon Kang
Publication date
01-12-2015
Publisher
BioMed Central
Published in
BMC Gastroenterology / Issue 1/2015
Electronic ISSN: 1471-230X
DOI
https://doi.org/10.1186/s12876-015-0349-4

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