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Published in: Pediatric Cardiology 6/2003

01-12-2003

Superoinferior Ventricles with Superior Left Ventricle and Inferior Right Ventricle: A Newly Recognized Form of Congenital Heart Disease

Authors: D. Porras, C. Kratz, M. Loukas, N. H. van Doesburg, A. Davignon, R. Van Praagh

Published in: Pediatric Cardiology | Issue 6/2003

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Abstract

We report the first known case of superoinferior ventricles with a superior morphologically left ventricle and an inferior morphologically right ventricle. This 2½-year-old boy also had dextrocardia, double-outlet right ventricle {S,L,L}, right-sided mitral atresia, left-sided tricuspid regurgitation, a large conoventricular type of ventricular septal defect, and pulmonary outflow tract stenosis. This very rare form of superoinferior ventricles appears to be due to excessive levorotation (≃170°) of discordant L-loop ventricles.
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Metadata
Title
Superoinferior Ventricles with Superior Left Ventricle and Inferior Right Ventricle: A Newly Recognized Form of Congenital Heart Disease
Authors
D. Porras
C. Kratz
M. Loukas
N. H. van Doesburg
A. Davignon
R. Van Praagh
Publication date
01-12-2003
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 6/2003
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-002-0396-9

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