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World Journal of Surgical Oncology

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Open Access 01-12-2006 | Case report

Sebaceous gland tumors and internal malignancy in the context of Muir-Torre syndrome. A case report and review of the literature

Authors: K Tsalis, K Blouhos, K Vasiliadis, T Tsachalis, S Angelopoulos, D Betsis

Published in: World Journal of Surgical Oncology | Issue 1/2006

Abstract

Background

The Muir-Torre syndrome is a rare autosomal dominant condition and is currently considered a subtype of the more common hereditary nonpolyposis colorectal cancer syndrome, in which multiple primary malignancies occur together with sebaceous gland tumors.

Case presentation

We describe a case of a 62-year-old woman with three primary colorectal tumors, genital tumor, and sebaceous adenomas and present her family history of three generations. Our case represents the first case reported from Greece in the international literature.

Conclusion

Recognition of the syndrome in patients with sebaceous gland tumors should facilitate early detection of subsequent malignancies if the patient is entered into appropriate screening programs.

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Title: Sebaceous gland tumors and internal malignancy in the context of Muir-Torre syndrome. A case report and review of the literature
Authors: K Tsalis
K Blouhos
K Vasiliadis
T Tsachalis
S Angelopoulos
D Betsis
Publication date: 01-12-2006
Publisher: BioMed Central
Published in: World Journal of Surgical Oncology / Issue 1/2006
Electronic ISSN: 1477-7819
DOI: https://doi.org/10.1186/1477-7819-4-8

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Sebaceous gland tumors and internal malignancy in the context of Muir-Torre syndrome. A case report and review of the literature

Abstract

Background

Case presentation

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Case presentation

Conclusion

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