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Clinical Rheumatology
Published in: Clinical Rheumatology 1/2007

01-01-2007 | Case Report

Retroperitoneal fibrosis and c-ANCA positivity

Authors: Clio P. Mavragani, Michalis Voulgarelis

Published in: Clinical Rheumatology | Issue 1/2007

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Abstract

Retroperitoneal fibrosis (RPF) is an uncommon collagen vascular disease characterized by a chronic nonspecific inflammation of the retroperitoneum, which can entrap and obstruct retroperitoneal structures. Although obscure, an autoimmune-mediated or vasculitic etiology has been hypothesized. In the current report, a case of RPF associated with the presence of antibodies against proteinase III, which responded effectively to immunosuppressive therapy, is presented.
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Metadata
Title
Retroperitoneal fibrosis and c-ANCA positivity
Authors
Clio P. Mavragani
Michalis Voulgarelis
Publication date
01-01-2007
Publisher
Springer-Verlag
Published in
Clinical Rheumatology / Issue 1/2007
Print ISSN: 0770-3198
Electronic ISSN: 1434-9949
DOI
https://doi.org/10.1007/s10067-005-0118-9

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