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Open Access 01-12-2013 | Case report

Progressive cyanosis following Kawashima operation: slow resolution after redirection of hepatic veins

Authors: Signe Holm Larsen, Kristian Emmertsen, Jesper Bjerre, Vibeke Elisabeth Hjortdal

Published in: Journal of Cardiothoracic Surgery | Issue 1/2013

Abstract

Progressive cyanosis often develops following Kawashima operation in patients with left atrial isomerism, interrupted inferior vena cava and hepatic veins draining to the atria. Knowledge on the timing and extend of resolution following hepatic venous redirection is sparse. A girl developed progressing cyanosis following Kawashima operation at the age of ten months. Arterial oxygen saturations at rest dropped to 60-65%. Surgical redirection of hepatic veins into the cavopulmonary circulation at the age of three years had no immediate effect. However, arterial oxygen saturations increased gradually over nine months to 90-93% and 95-100% after three years.

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Title: Progressive cyanosis following Kawashima operation: slow resolution after redirection of hepatic veins
Authors: Signe Holm Larsen
Kristian Emmertsen
Jesper Bjerre
Vibeke Elisabeth Hjortdal
Publication date: 01-12-2013
Publisher: BioMed Central
Published in: Journal of Cardiothoracic Surgery / Issue 1/2013
Electronic ISSN: 1749-8090
DOI: https://doi.org/10.1186/1749-8090-8-67

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Progressive cyanosis following Kawashima operation: slow resolution after redirection of hepatic veins

Abstract

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