Published in:
Open Access 01-12-2016 | Case
Primary adrenal leiomyosarcoma with lymph node metastasis: a case report
Published in: World Journal of Surgical Oncology | Issue 1/2016
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Background
Leiomyosarcomas typically originate in smooth muscle cell. Leiomyosarcoma potentially arising from the adrenal gland is an extremely rare mesenchymal tumors associated with delayed diagnosis and poor prognosis.
Case presentation
A 34-year-old man visited our department complaining of right hypochondriac pain. Computed tomography demonstrated a solid mass measuring 5.2 cm in diameter above the right kidney, corresponding to the right adrenal gland, and a lymph node mass, which appeared to have invaded the IVC wall. Right adrenalectomy and lymphadenectomy were performed. A microscopic examination revealed primary adrenal leiomyosarcoma with lymph node metastasis. No adjuvant therapy was performed, and the patient remains recurrence-free at 10 months postoperatively.
Conclusions
We experienced a very rare case of primary adrenal leiomyosarcoma.
Aggressive surgical resection including vascular reconstruction may be associated with improved survival.