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Pediatric Cardiology
Published in: Pediatric Cardiology 6/2011

01-08-2011 | Case Report

Preoperative Diagnosis of Long QT Syndrome in an Infant With Tetralogy of Fallot

Authors: Christoph P. Hornik, Michael J. Campbell, Michael P. Carboni, Andrew J. Lodge, John F. Rhodes Jr, Ronald J. Kanter

Published in: Pediatric Cardiology | Issue 6/2011

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Abstract

Long QT syndrome is a well-described entity in infants. Its presentation in the context of congenital heart disease is rare and is almost exclusively diagnosed postoperatively. For patients undergoing surgical intervention, preoperative knowledge of the diagnosis and appropriate perioperative management can be life-saving. We present the rare case of an infant with tetralogy of Fallot who was preoperatively diagnosed with long QT syndrome and discuss the implications of this diagnosis for his perioperative management.
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Metadata
Title
Preoperative Diagnosis of Long QT Syndrome in an Infant With Tetralogy of Fallot
Authors
Christoph P. Hornik
Michael J. Campbell
Michael P. Carboni
Andrew J. Lodge
John F. Rhodes Jr
Ronald J. Kanter
Publication date
01-08-2011
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 6/2011
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-011-9957-0

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