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Published in: Rheumatology International 10/2008

01-08-2008 | Case Report

Polyarteritis nodosa presenting as pancytopenia: case report and review of the literature

Authors: Leslie R. Harrold, Nancy Y. N. Liu

Published in: Rheumatology International | Issue 10/2008

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Abstract

Polyarteritis nodosa (PAN) is not commonly associated with hematologic abnormalities. We report the first case of pancytopenia as the presenting symptom of PAN. There was no associated malignancy or reactive hemophagocytic syndrome (RHS) to explain the findings. The patient, after successful treatment of PAN, subsequently developed RHS a few years later. He is the fourth reported case of RHS in a patient with PAN. In addition to describing the patient’s presentation and clinical course, a systematic review of the literature was performed examining the association between hematologic conditions, including RHS, and PAN.
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Metadata
Title
Polyarteritis nodosa presenting as pancytopenia: case report and review of the literature
Authors
Leslie R. Harrold
Nancy Y. N. Liu
Publication date
01-08-2008
Publisher
Springer-Verlag
Published in
Rheumatology International / Issue 10/2008
Print ISSN: 0172-8172
Electronic ISSN: 1437-160X
DOI
https://doi.org/10.1007/s00296-008-0572-1

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