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World Journal of Surgical Oncology
Published in: World Journal of Surgical Oncology 1/2014

Open Access 01-12-2014 | Case report

Perivascular epithelioid cell tumor of the rectum: report of a case and review of the literature

Authors: Amane Kanazawa, Shoichi Fujii, Ten-i Godai, Atsushi Ishibe, Takashi Oshima, Tadao Fukushima, Mitsuyoshi Ota, Norio Yukawa, Yasushi Rino, Toshio Imada, Junko Ito, Akinori Nozawa, Munetaka Masuda, Chikara Kunisaki

Published in: World Journal of Surgical Oncology | Issue 1/2014

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Abstract

We report a case of perivascular epithelioid cell tumor arising in the rectum of a 55-year-old woman. The tumor was treated by transanal endoscopic microsurgery. After 1 year follow-up, the patient is alive with no radiologic or endoscopic evidence of recurrence. Perivascular epithelioid cell tumor is a rare mesenchymal tumor characterized by co-expression of melanocytic and smooth muscle markers. This rare tumor can arise in various organs, including the falciform ligament, uterus, uterine cervix, liver, kidney, lung, breast, cardiac septum, pancreas, prostate, thigh, and gastrointestinal tract. Perivascular epithelioid cell tumor of the gastrointestinal tract is very rare, with only 23 previously reported cases. We review the literature on perivascular epithelioid cell tumors arising in the gastrointestinal tract.
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Metadata
Title
Perivascular epithelioid cell tumor of the rectum: report of a case and review of the literature
Authors
Amane Kanazawa
Shoichi Fujii
Ten-i Godai
Atsushi Ishibe
Takashi Oshima
Tadao Fukushima
Mitsuyoshi Ota
Norio Yukawa
Yasushi Rino
Toshio Imada
Junko Ito
Akinori Nozawa
Munetaka Masuda
Chikara Kunisaki
Publication date
01-12-2014
Publisher
BioMed Central
Published in
World Journal of Surgical Oncology / Issue 1/2014
Electronic ISSN: 1477-7819
DOI
https://doi.org/10.1186/1477-7819-12-12

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