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Pediatric Cardiology
Published in: Pediatric Cardiology 4/2007

01-08-2007 | CASE REPORT

Pentalogy of Cantrell Associated with Hypoplastic Left Heart Syndrome

Authors: D. S. Wheeler, J. D. St. Louis

Published in: Pediatric Cardiology | Issue 4/2007

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Abstract

Pentalogy of Cantrell is a rare anomaly characterized by midline closure defects, including a defect in the lower sternum, supraumbilical abdominal wall defect, deficiency of the anterior portion of the diaphragm, deficiency in the diaphragmatic portion of the pericardium with free communication between the pericardial and peritoneal cavities, and congenital heart defects. The long-term prognosis for children with this anomaly depends to a great extent on the complexity of the associated congenital heart defect. We describe the previously unreported association of pentalogy of Cantrell with hypoplastic left heart syndrome.
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Metadata
Title
Pentalogy of Cantrell Associated with Hypoplastic Left Heart Syndrome
Authors
D. S. Wheeler
J. D. St. Louis
Publication date
01-08-2007
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 4/2007
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-007-0016-9

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