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Pediatric Nephrology

Issue 1/2023

Content (36 Articles)

Editorial

A new team for the new year

Giovanni Montini, Joseph T. Flynn

Referees for 2022

Referees for 2022

Care Review

The learning health system for pediatric nephrology: building better systems to improve health

Charles D. Varnell Jr, Peter Margolis, Jens Goebel, David K. Hooper

Neonatal fluid overload—ignorance is no longer bliss

Lucinda J. Weaver, Colm P. Travers, Namasivayam Ambalavanan, David Askenazi

Hemolytic Uremic Syndrome Systematic Review/Meta-analysis

The treatment of atypical hemolytic uremic syndrome with eculizumab in pediatric patients: a systematic review

Raquel Medeiros de Souza, Bernardo Henrique Mendes Correa, Paulo Henrique Moreira Melo, Pedro Antunes Pousa, Tamires Sara Campos de Mendonça, Lucas Gustavo Castelar Rodrigues, Ana Cristina Simões e Silva

Open Access Nutrition Educational Review

Nutritional management of the infant with chronic kidney disease stages 2–5 and on dialysis

Vanessa Shaw, Caroline Anderson, An Desloovere, Larry A. Greenbaum, Dieter Haffner, Christina L. Nelms, Fabio Paglialonga, Nonnie Polderman, Leila Qizalbash, José Renken-Terhaerdt, Stella Stabouli, Jetta Tuokkola, Johan Vande Walle, Bradley A. Warady, Rukshana Shroff

Syphilis Clinical Quiz

A 16-month-old boy with nephrotic syndrome of apparent idiopathic origin: Question

Laura Beaudoin, Iris Puyol, Natalia Luján Robledo, Alejandro Balestracci

Syphilis Clinical Quiz

A 16-month-old boy with nephrotic syndrome of apparent idiopathic origin: Answer

Laura Beaudoin, Iris Puyol, Natalia Luján Robledo, Alejandro Balestracci

Hematuria Clinical Quiz

Unexpected finding in kidney biopsy of a child with nephrotic proteinuria: Questions

Meral Torun Bayram, Gizem Yildiz, Ahmet Okay Cağlayan, Ayfer Ulgenalp, Sadiye Mehtat Unlu, Alper Soylu, Salih Kavukcu

Clinical Quiz

Unexpected finding in kidney biopsy of a child with nephrotic proteinuria: Answers

Meral Torun Bayram, Gizem Yildiz, Ahmet Okay Cağlayan, Ayfer Ulgenalp, Sadiye Mehtat Unlu, Alper Soylu, Salih Kavukcu

Original Article

Clinical and genetic characteristics of Tunisian children with infantile nephropathic cystinosis

Mariem El Younsi, Médiha Trabelsi, Sandra Ben Youssef, Inès Ouertani, Yousra Hammi, Ahlem Achour, Faouzi Maazoul, Maher Kharrat, Tahar Gargah, Ridha M’rad

Septicemia Original Article

Epidemiology and outcomes of pneumococcal sepsis in children with nephrotic syndrome in a developing country

Georgie Mathew, Anish Sam George, R. V. Deepthi, Winsley Rose, Valsan Philip Verghese, Rosemol Varghese, Balaji Veeraraghavan, Indira Agarwal

Telemedicine Original Article

Dipping at home: is it better, easier, and more convenient? A feasibility and acceptability study of a novel home urinalysis using a smartphone application

Daniella Levy Erez, Hannah Derwick, Susan Furth, Lance Ballester, Stephanie Omuemu, Yonathan Adiri, Jonah Mink, Michelle Denburg

Open Access Abatacept Original Article

Benefit of B7-1 staining and abatacept for treatment-resistant post-transplant focal segmental glomerulosclerosis in a predominantly pediatric cohort: time for a reappraisal

George W. Burke III, Jayanthi Chandar, Junichiro Sageshima, Mariella Ortigosa-Goggins, Pooja Amarapurkar, Alla Mitrofanova, Marissa J. Defreitas, Chryso P. Katsoufis, Wacharee Seeherunvong, Alexandra Centeno, Javier Pagan, Lumen A. Mendez-Castaner, Adela D. Mattiazzi, Warren L. Kupin, Giselle Guerra, Linda J. Chen, Mahmoud Morsi, Jose M. G. Figueiro, Rodrigo Vianna, Carolyn L. Abitbol, David Roth, Alessia Fornoni, Phillip Ruiz, Gaetano Ciancio, Eduardo H. Garin

Urological Surgery Original Article

Congenital anomalies of the kidney and urinary tract (CAKUT) in critically ill infants: a multicenter cohort study

Esther Huimin Leow, Jan Hau Lee, Christoph P. Hornik, Yong Hong Ng, Thomas Hays, Reese H. Clark, Veeral N. Tolia, Rachel G. Greenberg

Kidney Injury Original Article

Kidney length standardized to body length predicts outcome in infants with a solitary functioning kidney

Douglas G. Matsell, Carol Bao, Teagan Po White, Ella Chan, Eli Matsell, Dan Cojocaru, Lydia Bajno, Marisa Catapang

SARS-CoV-2 Original Article

Outcomes and risk factors for death among hospitalized children and adolescents with kidney diseases and COVID-19: an analysis of a nationwide database

Mariana A. Vasconcelos, Ana Carmen Q. Mendonça, Enrico A. Colosimo, Noureddin Nourbakhsh, Hercílio Martelli-Júnior, Ludmila R. Silva, Maria Christina L. Oliveira, Clara C. Pinhati, Robert H. Mak, Ana Cristina Simões e Silva, Eduardo A. Oliveira

Type 1 Diabetes Original Article

Plasma levels of carboxylic acids are markers of early kidney dysfunction in young people with type 1 diabetes

Timothy Vigers, Carissa Vinovskis, Lu-Ping Li, Pottumarthi Prasad, Hiddo Heerspink, Angelo D’Alessandro, Julie A. Reisz, Federica Piani, David Z. Cherney, Daniel H. van Raalte, Kristen J. Nadeau, Meda E. Pavkov, Robert G. Nelson, Laura Pyle, Petter Bjornstad

Peritoneal Dialysis Original Article

Telehealth survey of providers and caregivers of children on peritoneal dialysis during the COVID-19 pandemic

Stephanie L. Clark, Brandy Begin, Heidi G. De Souza, Kathleen Mallett, Melisha G. Hanna, Troy Richardson, Megan Esporas, Ariana Bowie, Karri Taylor, Laura Castellanos Reyes, Monica Hughey, Alicia Neu, Bradley A. Warady

Peritonitis Original Article

An initiative to improve effluent culture detection among pediatric patients undergoing peritoneal dialysis through process improvement

Scott F. Pangonis, Joshua K. Schaffzin, Donna Claes, Joel E. Mortenson, Edward Nehus

Chronic Kidney Disease Original Article

Immature granulocytes as biomarkers of inflammation in children with predialysis chronic kidney disease

Nuran Cetın, Evin Kocaturk, Aslı Kavaz Tufan, Zeynep Kusku Kıraz, Ozkan Alatas

Open Access Original Article

Missing trial results: analysis of the current publication rate of studies in pediatric dialysis from 2003 to 2020

Christian Patry, Alexander Fichtner, Britta Höcker, Markus Ries, Claus Peter Schmitt, Burkhard Tönshoff

Chronic Kidney Disease Original Article

Improved equations to estimate GFR in Chinese children with chronic kidney disease

Ying Tang, Ling Hou, Tingting Sun, Shanping Li, Junli Cheng, Dan Xue, Xiuli Wang, Yue Du

Chronic Kidney Disease Original Article

Child and caregiver perspectives on access to psychosocial and educational support in pediatric chronic kidney disease: a focus group study

Yifan Zhang, Talia Gutman, Allison Tong, Jonathan C. Craig, Aditi Sinha, Allison Dart, Allison A. Eddy, Debbie S. Gipson, Detlef Bockenhauer, Hui-Kim Yap, Jaap Groothoff, Michael Zappitelli, Nicholas J.A.Webb, Stephen I. Alexander, Susan Furth, Susan Samuel, Tom D. Blydt-Hansen, Janis Dionne, Mini Michael, Scott E. Wenderfer, Wolfgang C. Winkelmayer, Steven McTaggart, Amanda Walker, Cortney T. Zimmerman, Angelique F. Ralph, Angela Ju, Laura J. James, Camilla S. Hanson

Peritoneal Dialysis Original Article

Survival analysis among pediatric patients receiving kidney replacement therapy: a Japanese nationwide cohort study

Daishi Hirano, Eisuke Inoue, Mayumi Sako, Akira Ashida, Masataka Honda, Shori Takahashi, Kazumoto Iijima, Motoshi Hattori

Kidney Transplantation Original Article

Assessment of the oral health status of children with chronic kidney disease

Berkant Sezer, Remziye Kaya, Nur Kodaman Dokumacıgil, Duygu Sıddıkoğlu, Serçin Güven, Nurdan Yıldız, Harika Alpay, Betül Kargül

Basiliximab Original Article

Early corticosteroid withdrawal is associated with improved adult height in pediatric kidney transplant recipients

Gilles Tourlamain, Mandy Keijzer-Veen, Antonia Bouts, Karlien Cransberg, Huib de Jong, Rani De Pauw, Karen Vanderstraeten, Amina El Amouri, Ann Raes, Noël Knops, Agnieszka Prytuła

Kidney Transplantation Original Article

Changes in graft function after living donor kidney transplantation in children

Junya Hashimoto, Yuko Hamasaki, Yujiro Aoki, Mai Kubota, Masaki Muramatsu, Takeshi Kawamura, Seiichiro Shishido, Ken Sakai

Myocarditis Brief Report

A child with crescentic glomerulonephritis following SARS-CoV-2 mRNA (Pfizer-BioNTech) vaccination

Sujeong Kim, Jiwon Jung, Haeyon Cho, Jina Lee, Heounjeong Go, Joo Hoon Lee

Peritoneal Dialysis Letter to the Editors

A rare cause of nephrotic syndrome – sphingosine-1-phosphate lyase (SGPL1) deficiency: 2 cases

Ana Paula Spizzirri, Carlos José Cobeñas, Angela del Carmen Suarez

Alport Syndrome Letter to the Editors

Response to Dr. Spizzirri et al

Tugba Tastemel Ozturk, Fatih Ozaltin, Rezan Topaloglu