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Published in: Pediatric Cardiology 2/2010

01-02-2010 | Case Report

Need for Comprehensive Vascular Assessment Before Surgical Repair of Aortic Coarctation in PHACES Syndrome

Authors: Alessandro Giardini, Caroline Gholam, Sachin Khambadkone, Martin Kostolny

Published in: Pediatric Cardiology | Issue 2/2010

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Abstract

Children with PHACES syndrome commonly present with aortic coarctation and abnormalities of the supra-aortic and intracranial arteries. We describe a case of complex aortic coarctation in the context of PHACES syndrome, where preoperative detection of abnormalities in supra-aortic and intracranial arteries led to modification of the surgical technique adopted, in order to avoid potential neurological damage.
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Metadata
Title
Need for Comprehensive Vascular Assessment Before Surgical Repair of Aortic Coarctation in PHACES Syndrome
Authors
Alessandro Giardini
Caroline Gholam
Sachin Khambadkone
Martin Kostolny
Publication date
01-02-2010
Publisher
Springer-Verlag
Published in
Pediatric Cardiology / Issue 2/2010
Print ISSN: 0172-0643
Electronic ISSN: 1432-1971
DOI
https://doi.org/10.1007/s00246-009-9592-1

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