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Clinical Rheumatology
Published in: Clinical Rheumatology 11/2022

12-08-2022 | Myelodysplastic Syndrome | Letters of Biomedical and Clinical Research

Kikuchi Fujimoto disease as the presenting component of VEXAS syndrome: a case report of a probable association

Authors: Umut Yılmaz, Sabriye Güner, Tuğçe Eşkazan, Ahu Senem Demiröz, Gözde Kurtuluş, Furkan Bahar, Serdal Uğurlu, Ahmet Emre Eşkazan

Published in: Clinical Rheumatology | Issue 11/2022

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Excerpt

Dear Editor, …
Literature
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Beck DB, Ferrada MA, Sikora KA, Ombrello AK, Collins JC, Pei W, et al (2020) Somatic mutations in UBA1 and severe adult-onset autoinflammatory disease. N Engl J Med [Internet]. Dec 31 [cited 2022 Mar 21];383(27):2628–38. Available from:  https://​pubmed.​ncbi.​nlm.​nih.​gov/​33108101/​. Accessed 20 March 2022
2.
Nune A, Iyengar KP, Barman B, Manzo C (2022) The VEXAS syndrome from rheumatology perspective: genomic DNA sequencing as available blueprint for diagnosing rheumatic diseases with overlapping haematological or dermatological findings [published online ahead of print, May 17]. Clin Rheumatol. 2022. https://​doi.​org/​10.​1007/​s10067-022-06211-1
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Lee SMS, Fan BE, Lim JHL, Goh LL, Lee JSS, Koh LW (2021) A case of VEXAS syndrome manifesting as Kikuchi-Fujimoto disease, relapsing polychondritis, venous thromboembolism and macrocytic anaemia. Rheumatology (Oxford, England) [Internet]. Sep 1 [cited 2022 Mar 21];60(9):E304–6. Available from: https://​pubmed.​ncbi.​nlm.​nih.​gov/​33630036/​. Accessed 20 March 2022
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Lin HC, Su CY, Huang CC, Hwang CF, Chien CY (2003) Kikuchi’s disease: a review and analysis of 61 cases. Otolaryngology--head and neck surgery : Off J Am Acad Otolaryngol-Head Neck Surg [Internet]. [cited 2022 Mar 21];128(5):650–3. Available from: https://​pubmed.​ncbi.​nlm.​nih.​gov/​12748557/​. Accessed 18 March 2022
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Kucukardali Y, Solmazgul E, Kunter E, Oncul O, Yildirim S, Kaplan M (2007) Kikuchi-Fujimoto disease: analysis of 244 cases. Clin Rheumatol 26(1):50–54CrossRef
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Anderson LA, Pfeiffer RM, Landgren O, Gadalla S, Berndt SI, Engels EA (2009) Risks of myeloid malignancies in patients with autoimmune conditions. Br J Cancer [Internet]. Mar 10 [cited 2022 Mar 21];100(5):822–8. Available from: https://​pubmed.​ncbi.​nlm.​nih.​gov/​19259097/​. Accessed 18 March 2022
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Yilmaz U, Ar MC, Esatoglu SN, Bavunoglu I, Erzin YZ, Hatemi AI, et al (2020) How to treat myelodysplastic syndrome with clinical features resembling Behçet syndrome: a case-based systematic review. Annals of hematology [Internet]. Jun 1 [cited 2022 Mar 21];99(6):1193–203. Available from: https://​pubmed.​ncbi.​nlm.​nih.​gov/​32140893/​. Accessed 6 July 2020
Metadata
Title
Kikuchi Fujimoto disease as the presenting component of VEXAS syndrome: a case report of a probable association
Authors
Umut Yılmaz
Sabriye Güner
Tuğçe Eşkazan
Ahu Senem Demiröz
Gözde Kurtuluş
Furkan Bahar
Serdal Uğurlu
Ahmet Emre Eşkazan
Publication date
12-08-2022
Publisher
Springer International Publishing
Published in
Clinical Rheumatology / Issue 11/2022
Print ISSN: 0770-3198
Electronic ISSN: 1434-9949
DOI
https://doi.org/10.1007/s10067-022-06331-8

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