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Journal of Medical Case Reports

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Open Access 01-12-2023 | Metastasis | Case report

Bilateral primary angiosarcoma of the breast: a case report

Authors: Yuka Ooe, Hirofumi Terakawa, Hiroko Kawashima, Hiroko Ikeda, Noriyuki Inaki

Published in: Journal of Medical Case Reports | Issue 1/2023

Abstract

Background

Primary angiosarcoma of the breast is very rare, accounting for 0.05% of all malignant breast tumors. It has very high malignant potential and poor prognosis, though due to the rarity of the disease, there is no established treatment. We report this case along with a literature review.

Case presentation

We report the case of a 30-year-old Asian woman who was diagnosed with bilateral primary angiosarcoma of the breast while breastfeeding. After surgery, she underwent radiation therapy, chemotherapy, and hepatic arterial infusion chemotherapy for local recurrence of liver metastases, but these were ineffective, and she required several arterial embolization procedures for intratumoral bleeding and rupture of liver metastases.

Conclusions

Angiosarcoma has a poor prognosis due to a high rate of local recurrence and distant metastasis. Although there is no established evidence for radiotherapy or chemotherapy, multimodality treatment may be necessary because of the high malignancy and rapid progression of the disease.

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Title: Bilateral primary angiosarcoma of the breast: a case report
Authors: Yuka Ooe
Hirofumi Terakawa
Hiroko Kawashima
Hiroko Ikeda
Noriyuki Inaki
Publication date: 01-12-2023
Publisher: BioMed Central
Keywords: Metastasis
Lactation
Cytostatic Therapy
Published in: Journal of Medical Case Reports / Issue 1/2023
Electronic ISSN: 1752-1947
DOI: https://doi.org/10.1186/s13256-023-03791-7

At a glance: The STEP trials

Springer Medicine

Bilateral primary angiosarcoma of the breast: a case report

Abstract

Background

Case presentation

Conclusions

At a glance: The STEP trials

Springer Medicine

Abstract

Background

Case presentation

Conclusions

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